Pulmonary Fibrosis and Interstitial Lung Disease ICD-10-CM codes

J84.10 is pulmonary fibrosis unspecified, covering post-inflammatory fibrosis and fibrosis of lung NOS. Idiopathic pulmonary fibrosis (J84.112) requires the provider to document IPF or usual interstitial pneumonia of idiopathic cause. The other idiopathic interstitial pneumonias are J84.111 (IIP not otherwise specified), J84.113 (nonspecific interstitial pneumonitis), J84.114 (acute interstitial pneumonitis), J84.115 (respiratory bronchiolitis ILD), J84.116 (cryptogenic organizing pneumonia), and J84.117 (desquamative interstitial pneumonia). ILD without further detail is J84.9.

ILD secondary to a systemic disease uses J84.170 (progressive fibrotic phenotype) or J84.178 (other fibrosing ILD in diseases classified elsewhere), with the underlying disease coded first: rheumatoid lung disease M05.1-, systemic sclerosis with lung involvement M34.81, or pulmonary sarcoidosis D86.0. J84 has a code-also note for any associated condition.

Drug-induced ILD (J70.2 acute, J70.3 chronic, J70.4 unspecified) is excluded from J84 and takes an additional adverse effect code for the drug. Pneumoconioses and hypersensitivity pneumonitis are classified to J60 to J67, for example asbestosis J61 and hypersensitivity pneumonitis J67.9. Add I27.23 for pulmonary hypertension due to lung disease, J96.1- for chronic respiratory failure, and Z99.81 for home oxygen dependence when documented.