Other interstitial pulmonary diseases
In Other respiratory diseases principally affecting the interstitium (J80-J84), chapter 10: Diseases of the Respiratory System
24 billable codes under J84: 6 are an MCC, 10 are a CC; 19 map to HCC 280 (Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders), HCC 278 (Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis).A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment. An HCC counts toward a Medicare Advantage patient's risk score.
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Instructional notes
Excludes1: not coded here, use a different code
- drug-induced interstitial lung disorders (J70.2-J70.4)
- interstitial emphysema (J98.2)
Excludes2: not included here, code separately if applicable
- lung diseases due to external agents (J60-J70)
Code also: add a code for this too, order depends on the encounter
- if applicable, associated condition
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers COPD and asthma exacerbations, sequencing of acute respiratory failure, confirmed versus suspected identified influenza, ventilator associated pneumonia, and vaping-related disorders.
- Chronic Obstructive Pulmonary Disease [COPD] and Asthma (page 56)
- Acute Respiratory Failure (page 56)
- Influenza due to certain identified influenza viruses (page 57)
- Ventilator associated Pneumonia (page 57)
- Vaping-related disorders (page 58)
All codes under J84
J84 can't be used on a claim. Pick a billable code below; grey headings group them.
- J84.0Alveolar and parieto-alveolar conditions
- J84.01Alveolar proteinosis
- J84.02Pulmonary alveolar microlithiasis
- J84.03Idiopathic pulmonary hemosiderosis
- J84.09Other alveolar and parieto-alveolar conditions
- J84.1Other interstitial pulmonary diseases with fibrosis
- J84.10Pulmonary fibrosis, unspecified
- J84.11Idiopathic interstitial pneumonia
- J84.111Idiopathic interstitial pneumonia, not otherwise specified
- J84.112Idiopathic pulmonary fibrosis
- J84.113Idiopathic non-specific interstitial pneumonitis
- J84.114Acute interstitial pneumonitis
- J84.115Respiratory bronchiolitis interstitial lung disease
- J84.116Cryptogenic organizing pneumonia
- J84.117Desquamative interstitial pneumonia
- J84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.2Lymphoid interstitial pneumonia
- J84.8Other specified interstitial pulmonary diseases
- J84.81Lymphangioleiomyomatosis
- J84.82Adult pulmonary Langerhans cell histiocytosis
- J84.83Surfactant mutations of the lung
- J84.84Other interstitial lung diseases of childhood
- J84.841Neuroendocrine cell hyperplasia of infancy
- J84.842Pulmonary interstitial glycogenosis
- J84.843Alveolar capillary dysplasia with vein misalignment
- J84.848Other interstitial lung diseases of childhood
- J84.89Other specified interstitial pulmonary diseases
- J84.9Interstitial pulmonary disease, unspecified
J84 MS-DRGs
As the principal diagnosis, the billable codes under J84 group to MS-DRG 196, 197, 198, 791, or 793 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 196 Interstitial Lung Disease with MCC (24 of 24 codes)
- DRG 197 Interstitial Lung Disease with CC (24 of 24 codes)
- DRG 198 Interstitial Lung Disease without CC/MCC (24 of 24 codes)
- DRG 791 Prematurity with Major Problems (5 of 24 codes)
- DRG 793 Full Term Neonate with Major Problems (5 of 24 codes)
Other codes that refer to J84
Notes on these codes point to J84.
- I27.23 Code Also: interstitial lung disease (J84.-)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Interstitial Lung Diseases
Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.
Read more about interstitial lung diseases on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
