Nephrotic Syndrome ICD-10-CM codes
ICD-10-CM codes for nephrotic syndrome by kidney biopsy finding, including minimal change disease, FSGS, and membranous nephropathy.
22 codes, 19 billable. FY2027, valid from October 1, 2026. In chapter 14: Diseases of the Genitourinary System.
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How to code Nephrotic Syndrome
Nephrotic syndrome is coded to N04 with a fourth character for the morphology seen on biopsy. N04.0 is minimal change disease, N04.1 is focal segmental glomerulosclerosis (FSGS), N04.2- is membranous (N04.21 primary, N04.22 secondary membranous nephropathy), and N04.9 is used when the morphology is not documented.
Nephrotic syndrome due to diabetes is reported with the diabetic kidney code, such as E11.21, and lupus nephritis is M32.14. Proteinuria without a diagnosis of nephrotic syndrome is R80.-.
All Nephrotic Syndrome codes
- E11.21Type 2 diabetes mellitus with diabetic nephropathy
- M32.14Glomerular disease in systemic lupus erythematosus
- N04Nephrotic syndrome
- N04.0Nephrotic syndrome with minor glomerular abnormality
- N04.1Nephrotic syndrome with focal and segmental glomerular lesions
- N04.2Nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.20Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
- N04.21Primary membranous nephropathy with nephrotic syndrome
- N04.22Secondary membranous nephropathy with nephrotic syndrome
- N04.29Other nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
- N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
- N04.6Nephrotic syndrome with dense deposit disease
- N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritis
- N04.8Nephrotic syndrome with other morphologic changes
- N04.9Nephrotic syndrome with unspecified morphologic changes
- N04.ANephrotic syndrome with C3 glomerulonephritis
- N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B1Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B2Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- R80.9Proteinuria, unspecified
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