N04

Non-Billable
ChapterN00–N99
Rankcategory
Official Description

Nephrotic syndrome

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 14: Diseases of the Genitourinary System (N00-N99).

CH14 Parent Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

N00-N08 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • hypertensive chronic kidney disease (I12.-)
Code Also
  • any associated kidney failure (N17-N19).

Instructional Notes

Includes
  • congenital nephrotic syndrome
  • lipoid nephrosis

Clinical Hierarchy

BillableHas subcodes
CH14Diseases of the genitourinary system (N00-N99)
N00-N08Glomerular diseases (N00-N08)
N04Nephrotic syndromeNot billable
N04.0Nephrotic syndrome with minor glomerular abnormalityBillable
N04.1Nephrotic syndrome with focal and segmental glomerular lesionsBillable
N04.2Nephrotic syndrome with diffuse membranous glomerulonephritisSubcodes
N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
N04.6Nephrotic syndrome with dense deposit diseaseBillable
N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritisBillable
N04.8Nephrotic syndrome with other morphologic changesBillable
N04.9Nephrotic syndrome with unspecified morphologic changesBillable
N04.ANephrotic syndrome with C3 glomerulonephritisBillable
N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)Subcodes

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to N04:

blockN00-N08
Glomerular diseases (N00-N08)
View context instructions
chapterCH14
Diseases of the genitourinary system (N00-N99)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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