Nephrotic syndrome
In Glomerular diseases (N00-N08), chapter 14: Diseases of the Genitourinary System
16 billable codes under N04: all are a CC; none map to an HCC.A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment.
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Instructional notes
Includes: conditions that are coded here
- congenital nephrotic syndrome
- lipoid nephrosis
Also applies, from Glomerular diseases (N00-N08)
These notes sit on N00-N08 and apply to every code under it, including N04.
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers chronic kidney disease staging, CKD in kidney transplant patients, and sequencing CKD with related conditions such as diabetes and hypertension.
- Chronic kidney disease (page 62)
All codes under N04
N04 can't be used on a claim. Pick a billable code below; grey headings group them.
- N04.0Nephrotic syndrome with minor glomerular abnormality
- N04.1Nephrotic syndrome with focal and segmental glomerular lesions
- N04.2Nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.20Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
- N04.21Primary membranous nephropathy with nephrotic syndrome
- N04.22Secondary membranous nephropathy with nephrotic syndrome
- N04.29Other nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
- N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
- N04.6Nephrotic syndrome with dense deposit disease
- N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritis
- N04.8Nephrotic syndrome with other morphologic changes
- N04.9Nephrotic syndrome with unspecified morphologic changes
- N04.ANephrotic syndrome with C3 glomerulonephritis
- N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B1Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B2Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
N04 MS-DRGs
As the principal diagnosis, all 16 billable codes under N04 group to MS-DRG 698, 699, or 700 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
Other codes that refer to N04
Notes on these codes point to N04.
- Q63 Excludes1: congenital nephrotic syndrome (N04.-)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Kidney Diseases
You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.
Read more about kidney diseases on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.