Interstitial Lung Disease ICD-10-CM codes
ICD-10-CM codes for interstitial lung disease (ILD), including idiopathic interstitial pneumonias, drug-induced ILD, hypersensitivity pneumonitis, and ILD in connective tissue disease.
39 codes, 32 billable. FY2027, valid from October 1, 2026. In chapter 10: Diseases of the Respiratory System.
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How to code Interstitial Lung Disease
J84.9 is interstitial pulmonary disease, unspecified, and is the code for ILD NOS. Idiopathic pulmonary fibrosis is J84.112, nonspecific interstitial pneumonitis is J84.113, and cryptogenic organizing pneumonia is J84.116. Pulmonary fibrosis without a stated type is J84.10; see the pulmonary fibrosis guide.
Drug-induced ILD is coded from J70.2 (acute), J70.3 (chronic), or J70.4 (unspecified), with the drug's adverse effect code added. Hypersensitivity pneumonitis is coded from J67, for example J67.9 when the dust is not specified.
ILD from a connective tissue disease uses the combination code for that disease, such as M34.81 for systemic sclerosis, M05.10 for rheumatoid lung disease, or M35.02 for Sjogren syndrome. Progressive fibrosing ILD in these diseases adds J84.170. Pulmonary sarcoidosis is D86.0.
All Interstitial Lung Disease codes
- D86.0Sarcoidosis of lung
- J67.9Hypersensitivity pneumonitis due to unspecified organic dust
- J70.2Acute drug-induced interstitial lung disorders
- J70.3Chronic drug-induced interstitial lung disorders
- J70.4Drug-induced interstitial lung disorders, unspecified
- J84Other interstitial pulmonary diseases
- J84.0Alveolar and parieto-alveolar conditions
- J84.01Alveolar proteinosis
- J84.02Pulmonary alveolar microlithiasis
- J84.03Idiopathic pulmonary hemosiderosis
- J84.09Other alveolar and parieto-alveolar conditions
- J84.1Other interstitial pulmonary diseases with fibrosis
- J84.10Pulmonary fibrosis, unspecified
- J84.11Idiopathic interstitial pneumonia
- J84.111Idiopathic interstitial pneumonia, not otherwise specified
- J84.112Idiopathic pulmonary fibrosis
- J84.113Idiopathic non-specific interstitial pneumonitis
- J84.114Acute interstitial pneumonitis
- J84.115Respiratory bronchiolitis interstitial lung disease
- J84.116Cryptogenic organizing pneumonia
- J84.117Desquamative interstitial pneumonia
- J84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.2Lymphoid interstitial pneumonia
- J84.8Other specified interstitial pulmonary diseases
- J84.81Lymphangioleiomyomatosis
- J84.82Adult pulmonary Langerhans cell histiocytosis
- J84.83Surfactant mutations of the lung
- J84.84Other interstitial lung diseases of childhood
- J84.841Neuroendocrine cell hyperplasia of infancy
- J84.842Pulmonary interstitial glycogenosis
- J84.843Alveolar capillary dysplasia with vein misalignment
- J84.848Other interstitial lung diseases of childhood
- J84.89Other specified interstitial pulmonary diseases
- J84.9Interstitial pulmonary disease, unspecified
- M05.10Rheumatoid lung disease with rheumatoid arthritis of unspecified site
- M34.81Systemic sclerosis with lung involvement
- M35.02Sjögren syndrome with lung involvement
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