Pulmonary Hypertension ICD-10-CM codes
ICD-10-CM codes for pulmonary hypertension by WHO group, including primary pulmonary arterial hypertension, pulmonary hypertension due to left heart or lung disease, and CTEPH.
14 codes, 13 billable. FY2027, valid from October 1, 2026. In chapter 9: Diseases of the Circulatory System.
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How to code Pulmonary Hypertension
I27.20 is pulmonary hypertension, unspecified. Primary (idiopathic) pulmonary arterial hypertension is I27.0. The other codes follow the WHO groups: I27.21 secondary pulmonary arterial hypertension (group 1), I27.22 due to left heart disease (group 2), I27.23 due to lung disease and hypoxia (group 3), I27.24 chronic thromboembolic pulmonary hypertension (group 4), and I27.29 other secondary types (group 5).
Code the underlying condition as well when it is documented, such as heart failure I50.- with I27.22, or COPD J44.9 with I27.23. Add Z99.81 for dependence on supplemental oxygen.
Chronic cor pulmonale is I27.81 and Eisenmenger syndrome is I27.83. Pulmonary hypertension of the newborn is P29.30.
All Pulmonary Hypertension codes
- I27.0Primary pulmonary hypertension
- I27.2Other secondary pulmonary hypertension
- I27.20Pulmonary hypertension, unspecified
- I27.21Secondary pulmonary arterial hypertension
- I27.22Pulmonary hypertension due to left heart disease
- I27.23Pulmonary hypertension due to lung diseases and hypoxia
- I27.24Chronic thromboembolic pulmonary hypertension
- I27.29Other secondary pulmonary hypertension
- I27.81Cor pulmonale (chronic)
- I27.83Eisenmenger's syndrome
- I50.9Heart failure, unspecified
- J44.9Chronic obstructive pulmonary disease, unspecified
- P29.30Pulmonary hypertension of newborn
- Z99.81Dependence on supplemental oxygen
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