Pulmonary Hypertension ICD-10-CM codes

ICD-10-CM codes for pulmonary hypertension by WHO group, including primary pulmonary arterial hypertension, pulmonary hypertension due to left heart or lung disease, and CTEPH.

14 codes, 13 billable. FY2027, valid from October 1, 2026. In chapter 9: Diseases of the Circulatory System.

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How to code Pulmonary Hypertension

I27.20 is pulmonary hypertension, unspecified. Primary (idiopathic) pulmonary arterial hypertension is I27.0. The other codes follow the WHO groups: I27.21 secondary pulmonary arterial hypertension (group 1), I27.22 due to left heart disease (group 2), I27.23 due to lung disease and hypoxia (group 3), I27.24 chronic thromboembolic pulmonary hypertension (group 4), and I27.29 other secondary types (group 5).

Code the underlying condition as well when it is documented, such as heart failure I50.- with I27.22, or COPD J44.9 with I27.23. Add Z99.81 for dependence on supplemental oxygen.

Chronic cor pulmonale is I27.81 and Eisenmenger syndrome is I27.83. Pulmonary hypertension of the newborn is P29.30.

All Pulmonary Hypertension codes

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