Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Internal Codes
  • E83.19|

    Other disorders of iron metabolism

  • E83.2|

    Disorders of zinc metabolism

  • E83.3|

    Disorders of phosphorus metabolism and phosphatases

  • E83.30|

    Disorder of phosphorus metabolism, unspecified

  • E83.31|

    Familial hypophosphatemia

  • E83.32|

    Hereditary vitamin D-dependent rickets (type 1) (type 2)

  • E83.39|

    Other disorders of phosphorus metabolism

  • E83.4|

    Disorders of magnesium metabolism

  • E83.40|

    Disorders of magnesium metabolism, unspecified

  • E83.41|

    Hypermagnesemia

  • E83.42|

    Hypomagnesemia

  • E83.49|

    Other disorders of magnesium metabolism

  • E83.5|

    Disorders of calcium metabolism

  • E83.50|

    Unspecified disorder of calcium metabolism

  • E83.51|

    Hypocalcemia

  • E83.52|

    Hypercalcemia

  • E83.59|

    Other disorders of calcium metabolism

  • E83.8|

    Other disorders of mineral metabolism

  • E83.81|

    Hungry bone syndrome

  • E83.82|

    Disorders of pyrophosphate metabolism

  • E83.820|

    Generalized arterial calcification of infancy with unspecified genetic causality

  • E83.821|

    ENPP1 deficiency causing generalized arterial calcification of infancy

  • E83.822|

    ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

  • E83.823|

    ABCC6 deficiency causing generalized arterial calcification of infancy

  • E83.824|

    ABCC6 deficiency causing pseudoxanthoma elasticum

  • E83.825|

    CD73 deficiency causing arterial calcification

  • E83.89|

    Other disorders of mineral metabolism

  • E83.9|

    Disorder of mineral metabolism, unspecified

  • E84|

    Cystic fibrosis

  • E84.0|

    Cystic fibrosis with pulmonary manifestations

  • E84.1|

    Cystic fibrosis with intestinal manifestations

  • E84.11|

    Meconium ileus in cystic fibrosis

  • E84.19|

    Cystic fibrosis with other intestinal manifestations

  • E84.8|

    Cystic fibrosis with other manifestations

  • E84.9|

    Cystic fibrosis, unspecified

  • E85|

    Amyloidosis

  • E85.0|

    Non-neuropathic heredofamilial amyloidosis

  • E85.1|

    Neuropathic heredofamilial amyloidosis

  • E85.2|

    Heredofamilial amyloidosis, unspecified

  • E85.3|

    Secondary systemic amyloidosis

  • E85.4|

    Organ-limited amyloidosis

  • E85.8|

    Other amyloidosis

  • E85.81|

    Light chain (AL) amyloidosis

  • E85.82|

    Wild-type transthyretin-related (ATTR) amyloidosis

  • E85.89|

    Other amyloidosis

  • E85.9|

    Amyloidosis, unspecified

  • E86|

    Volume depletion

  • E86.0|

    Dehydration

  • E86.1|

    Hypovolemia

  • E86.9|

    Volume depletion, unspecified

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