E85.0

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Non-neuropathic heredofamilial amyloidosis

Metadata & Insights
  • Billable/specific code (valid for reimbursement).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Hereditary amyloid nephropathy
Excludes2(Not included here. Code separately if applicable.)
  • Transthyretin-related (ATTR) familial amyloid cardiomyopathy (E85.4)
Code Also
  • associated disorders, such as:
  • autoinflammatory syndromes (M04.-)
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E85Amyloidosis
E85.0Non-neuropathic heredofamilial amyloidosisBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E85.0:

categoryE85
Amyloidosis
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Code History

  • FY 2016: Superseded by M04.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

Cross Reference

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