Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Internal Codes
  • E00

    Congenital iodine-deficiency syndrome

  • E00.0

    Congenital iodine-deficiency syndrome, neurological type

  • E00.1

    Congenital iodine-deficiency syndrome, myxedematous type

  • E00.2

    Congenital iodine-deficiency syndrome, mixed type

  • E00.9

    Congenital iodine-deficiency syndrome, unspecified

  • E01

    Iodine-deficiency related thyroid disorders and allied conditions

  • E01.0

    Iodine-deficiency related diffuse (endemic) goiter

  • E01.1

    Iodine-deficiency related multinodular (endemic) goiter

  • E01.2

    Iodine-deficiency related (endemic) goiter, unspecified

  • E01.8

    Other iodine-deficiency related thyroid disorders and allied conditions

  • E02

    Subclinical iodine-deficiency hypothyroidism

  • E03

    Other hypothyroidism

  • E03.0

    Congenital hypothyroidism with diffuse goiter

  • E03.1

    Congenital hypothyroidism without goiter

  • E03.2

    Hypothyroidism due to medicaments and other exogenous substances

  • E03.3

    Postinfectious hypothyroidism

  • E03.4

    Atrophy of thyroid (acquired)

  • E03.5

    Myxedema coma

  • E03.8

    Other specified hypothyroidism

  • E03.9

    Hypothyroidism, unspecified

  • E04

    Other nontoxic goiter

  • E04.0

    Nontoxic diffuse goiter

  • E04.1

    Nontoxic single thyroid nodule

  • E04.2

    Nontoxic multinodular goiter

  • E04.8

    Other specified nontoxic goiter

  • E04.9

    Nontoxic goiter, unspecified

  • E05

    Thyrotoxicosis [hyperthyroidism]

  • E05.0

    Thyrotoxicosis with diffuse goiter

  • E05.00

    Thyrotoxicosis with diffuse goiter without thyrotoxic crisis or storm

  • E05.01

    Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm

  • E05.1

    Thyrotoxicosis with toxic single thyroid nodule

  • E05.10

    Thyrotoxicosis with toxic single thyroid nodule without thyrotoxic crisis or storm

  • E05.11

    Thyrotoxicosis with toxic single thyroid nodule with thyrotoxic crisis or storm

  • E05.2

    Thyrotoxicosis with toxic multinodular goiter

  • E05.20

    Thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis or storm

  • E05.21

    Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis or storm

  • E05.3

    Thyrotoxicosis from ectopic thyroid tissue

  • E05.30

    Thyrotoxicosis from ectopic thyroid tissue without thyrotoxic crisis or storm

  • E05.31

    Thyrotoxicosis from ectopic thyroid tissue with thyrotoxic crisis or storm

  • E05.4

    Thyrotoxicosis factitia

  • E05.40

    Thyrotoxicosis factitia without thyrotoxic crisis or storm

  • E05.41

    Thyrotoxicosis factitia with thyrotoxic crisis or storm

  • E05.8

    Other thyrotoxicosis

  • E05.80

    Other thyrotoxicosis without thyrotoxic crisis or storm

  • E05.81

    Other thyrotoxicosis with thyrotoxic crisis or storm

  • E05.9

    Thyrotoxicosis, unspecified

  • E05.90

    Thyrotoxicosis, unspecified without thyrotoxic crisis or storm

  • E05.91

    Thyrotoxicosis, unspecified with thyrotoxic crisis or storm

  • E06

    Thyroiditis

  • E06.0

    Acute thyroiditis

Page 1 of 21Next