E00–E89: Endocrine, Nutritional and Metabolic Diseases
Chapter 4 of ICD-10-CM 2027, 1,270 codes in 10 blocks.
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Chapter instructions
Excludes1: not coded here, use a different code
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Codes in this chapter
All codesBillable only1,270 results
- E78.1Pure hyperglyceridemia
- E78.2Mixed hyperlipidemia
- E78.3Hyperchylomicronemia
- E78.4Other hyperlipidemia
- E78.41Elevated Lipoprotein(a)
- E78.49Other hyperlipidemia
- E78.5Hyperlipidemia, unspecified
- E78.6Lipoprotein deficiency
- E78.7Disorders of bile acid and cholesterol metabolism
- E78.70Disorder of bile acid and cholesterol metabolism, unspecified
- E78.71Barth syndrome
- E78.72Smith-Lemli-Opitz syndrome
- E78.79Other disorders of bile acid and cholesterol metabolism
- E78.8Other disorders of lipoprotein metabolism
- E78.81Lipoid dermatoarthritis
- E78.89Other lipoprotein metabolism disorders
- E78.9Disorder of lipoprotein metabolism, unspecified
- E79Disorders of purine and pyrimidine metabolism
- E79.0Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
- E79.1Lesch-Nyhan syndrome
- E79.2Myoadenylate deaminase deficiency
- E79.8Other disorders of purine and pyrimidine metabolism
- E79.81Aicardi-Goutieres syndrome
- E79.82Hereditary xanthinuria
- E79.89Other specified disorders of purine and pyrimidine metabolism
- E79.9Disorder of purine and pyrimidine metabolism, unspecified
- E80Disorders of porphyrin and bilirubin metabolism
- E80.0Hereditary erythropoietic porphyria
- E80.1Porphyria cutanea tarda
- E80.2Other and unspecified porphyria
- E80.20Unspecified porphyria
- E80.21Acute intermittent (hepatic) porphyria
- E80.29Other porphyria
- E80.3Defects of catalase and peroxidase
- E80.4Gilbert syndrome
- E80.5Crigler-Najjar syndrome
- E80.6Other disorders of bilirubin metabolism
- E80.7Disorder of bilirubin metabolism, unspecified
- E83Disorders of mineral metabolism
- E83.0Disorders of copper metabolism
- E83.00Disorder of copper metabolism, unspecified
- E83.01Wilson's disease
- E83.09Other disorders of copper metabolism
- E83.1Disorders of iron metabolism
- E83.10Disorder of iron metabolism, unspecified
- E83.11Hemochromatosis
- E83.110Hereditary hemochromatosis
- E83.111Hemochromatosis due to repeated red blood cell transfusions
- E83.118Other hemochromatosis
- E83.119Hemochromatosis, unspecified
