All ICD10 Codes
E80Non-billable

Disorders of porphyrin and bilirubin metabolism

Endocrine, Nutritional and Metabolic Diseases·Metabolic disorders (E70-E88)·category·FY 2026

Use a more specific code (7 billable, 1 non-billable)
E80.0Hereditary erythropoietic porphyriaE80.1Porphyria cutanea tardaE80.2Other and unspecified porphyriahas subcodesE80.3Defects of catalase and peroxidaseE80.4Gilbert syndromeE80.5Crigler-Najjar syndromeE80.6Other disorders of bilirubin metabolismE80.7Disorder of bilirubin metabolism, unspecified

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Instructional Notes

Includes
  • defects of catalase and peroxidase

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E80Disorders of porphyrin and bilirubin metabolismNot billable
E80.0Hereditary erythropoietic porphyriaBillable
E80.1Porphyria cutanea tardaBillable
E80.2Other and unspecified porphyriaSubcodes
E80.3Defects of catalase and peroxidaseBillable
E80.4Gilbert syndromeBillable
E80.5Crigler-Najjar syndromeBillable
E80.6Other disorders of bilirubin metabolismBillable
E80.7Disorder of bilirubin metabolism, unspecifiedBillable

MS-DRG Classification

2026

No direct MS-DRG triggers identified.