All ICD10 Codes

E78.71

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Barth syndrome

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E78 NotesView E78.7 Notes

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E78Disorders of lipoprotein metabolism and other lipidemias
E78.7Disorders of bile acid and cholesterol metabolism
E78.71Barth syndromeBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E78.71:

subcategoryE78.7
Disorders of bile acid and cholesterol metabolism
View context instructions
categoryE78
Disorders of lipoprotein metabolism and other lipidemias
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 564
Other Musculoskeletal System and Connective Tissue Diagnoses with MCC
DRG 565
Other Musculoskeletal System and Connective Tissue Diagnoses with CC
DRG 566
Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC

Cross Reference

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