Disorders of lipoprotein metabolism and other lipidemias
In Metabolic disorders (E70-E88), chapter 4: Endocrine, Nutritional and Metabolic Diseases
18 billable codes under E78: 2 are a CC; none map to an HCC.A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment.
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Instructional notes
Excludes1: not coded here, use a different code
- sphingolipidosis (E75.0-E75.3)
Also applies, from Metabolic disorders (E70-E88)
These notes sit on E70-E88 and apply to every code under it, including E78.
Excludes1: not coded here, use a different code
Excludes2: not included here, code separately if applicable
- Ehlers-Danlos syndromes (Q79.6-)
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers diabetes mellitus coding, including type, insulin and drug use, pump malfunction and secondary diabetes, plus obesity and obesity class codes.
- Diabetes mellitus (page 39)
- Obesity (page 42)
All codes under E78
E78 can't be used on a claim. Pick a billable code below; grey headings group them.
- E78.0Pure hypercholesterolemia
- E78.00Pure hypercholesterolemia, unspecified
- E78.01Familial hypercholesterolemia
- E78.010Homozygous familial hypercholesterolemia [HoFH]
- E78.011Heterozygous familial hypercholesterolemia [HeFH]
- E78.019Familial hypercholesterolemia, unspecified
- E78.1Pure hyperglyceridemia
- E78.2Mixed hyperlipidemia
- E78.3Hyperchylomicronemia
- E78.4Other hyperlipidemia
- E78.41Elevated Lipoprotein(a)
- E78.49Other hyperlipidemia
- E78.5Hyperlipidemia, unspecified
- E78.6Lipoprotein deficiency
- E78.7Disorders of bile acid and cholesterol metabolism
- E78.70Disorder of bile acid and cholesterol metabolism, unspecified
- E78.71Barth syndrome
- E78.72Smith-Lemli-Opitz syndrome
- E78.79Other disorders of bile acid and cholesterol metabolism
- E78.8Other disorders of lipoprotein metabolism
- E78.81Lipoid dermatoarthritis
- E78.89Other lipoprotein metabolism disorders
- E78.9Disorder of lipoprotein metabolism, unspecified
E78 MS-DRGs
As the principal diagnosis, the billable codes under E78 group to MS-DRG 642, 564, 565, or 566 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 642 Inborn and Other Disorders of Metabolism (16 of 18 codes)
- DRG 564 Other Musculoskeletal System and Connective Tissue Diagnoses with MCC (2 of 18 codes)
- DRG 565 Other Musculoskeletal System and Connective Tissue Diagnoses with CC (2 of 18 codes)
- DRG 566 Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC (2 of 18 codes)
Other codes that refer to E78
Notes on these codes point to E78.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Lipid Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.
Read more about lipid metabolism disorders on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.