All ICD10 Codes

E78.011

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Heterozygous familial hypercholesterolemia [HeFH]

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E78 Notes

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E78Disorders of lipoprotein metabolism and other lipidemias
E78.0Pure hypercholesterolemia
E78.01Familial hypercholesterolemia
E78.011Heterozygous familial hypercholesterolemia [HeFH]Billable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E78.011:

categoryE78
Disorders of lipoprotein metabolism and other lipidemias
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Code History

  • FY 2025: This code replaced E78.01 (Familial hypercholesterolemia)

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

Find Procedures (ICD-10-PCS)

Find surgical and procedural codes related to Heterozygous familial hypercholesterolemia [HeFH].

Search PCS Codes