E84

Non-Billable
ChapterE00–E89
Rankcategory
Official Description

Cystic fibrosis

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Instructional Notes

Includes
  • mucoviscidosis
Code Also
  • exocrine pancreatic insufficiency (K86.81)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E84Cystic fibrosisNot billable
E84.0Cystic fibrosis with pulmonary manifestationsBillable
E84.1Cystic fibrosis with intestinal manifestationsSubcodes
E84.8Cystic fibrosis with other manifestationsBillable
E84.9Cystic fibrosis, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E84:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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