E00–E89: Endocrine, Nutritional and Metabolic Diseases
Chapter 4 of ICD-10-CM 2027, 1,270 codes in 10 blocks.
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Chapter instructions
Excludes1: not coded here, use a different code
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Codes in this chapter
All codesBillable only1,270 results
- E71.510Zellweger syndrome
- E71.511Neonatal adrenoleukodystrophy
- E71.518Other disorders of peroxisome biogenesis
- E71.52X-linked adrenoleukodystrophy
- E71.520Childhood cerebral X-linked adrenoleukodystrophy
- E71.521Adolescent X-linked adrenoleukodystrophy
- E71.522Adrenomyeloneuropathy
- E71.528Other X-linked adrenoleukodystrophy
- E71.529X-linked adrenoleukodystrophy, unspecified type
- E71.53Other group 2 peroxisomal disorders
- E71.54Other peroxisomal disorders
- E71.540Rhizomelic chondrodysplasia punctata
- E71.541Zellweger-like syndrome
- E71.542Other group 3 peroxisomal disorders
- E71.548Other peroxisomal disorders
- E72Other disorders of amino-acid metabolism
- E72.0Disorders of amino-acid transport
- E72.00Disorders of amino-acid transport, unspecified
- E72.01Cystinuria
- E72.02Hartnup's disease
- E72.03Lowe's syndrome
- E72.04Cystinosis
- E72.09Other disorders of amino-acid transport
- E72.1Disorders of sulfur-bearing amino-acid metabolism
- E72.10Disorders of sulfur-bearing amino-acid metabolism, unspecified
- E72.11Homocystinuria
- E72.12Methylenetetrahydrofolate reductase deficiency
- E72.19Other disorders of sulfur-bearing amino-acid metabolism
- E72.2Disorders of urea cycle metabolism
- E72.20Disorder of urea cycle metabolism, unspecified
- E72.21Argininemia
- E72.22Arginosuccinic aciduria
- E72.23Citrullinemia
- E72.29Other disorders of urea cycle metabolism
- E72.3Disorders of lysine and hydroxylysine metabolism
- E72.4Disorders of ornithine metabolism
- E72.5Disorders of glycine metabolism
- E72.50Disorder of glycine metabolism, unspecified
- E72.51Non-ketotic hyperglycinemia
- E72.52Trimethylaminuria
- E72.53Primary hyperoxaluria
- E72.530Primary hyperoxaluria, type 1
- E72.538Other specified primary hyperoxaluria
- E72.539Primary hyperoxaluria, unspecified
- E72.54Secondary hyperoxaluria
- E72.540Dietary hyperoxaluria
- E72.541Enteric hyperoxaluria
- E72.548Other secondary hyperoxaluria
- E72.549Secondary hyperoxaluria, unspecified
- E72.59Other disorders of glycine metabolism
