Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)

transitory endocrine and metabolic disorders specific to newborn (P70-P74)

All Codes Billable Only

Internal Codes

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E72.8|
Other specified disorders of amino-acid metabolism
E72.81|
Disorders of gamma aminobutyric acid metabolism
E72.89|
Other specified disorders of amino-acid metabolism
E72.9|
Disorder of amino-acid metabolism, unspecified
E73|
Lactose intolerance
E73.0|
Congenital lactase deficiency
E73.1|
Secondary lactase deficiency
E73.8|
Other lactose intolerance
E73.9|
Lactose intolerance, unspecified
E74|
Other disorders of carbohydrate metabolism
E74.0|
Glycogen storage disease
E74.00|
Glycogen storage disease, unspecified
E74.01|
von Gierke disease
E74.02|
Pompe disease
E74.03|
Cori disease
E74.04|
McArdle disease
E74.05|
Lysosome-associated membrane protein 2 [LAMP2] deficiency
E74.09|
Other glycogen storage disease
E74.1|
Disorders of fructose metabolism
E74.10|
Disorder of fructose metabolism, unspecified
E74.11|
Essential fructosuria
E74.12|
Hereditary fructose intolerance
E74.19|
Other disorders of fructose metabolism
E74.2|
Disorders of galactose metabolism
E74.20|
Disorders of galactose metabolism, unspecified
E74.21|
Galactosemia
E74.29|
Other disorders of galactose metabolism
E74.3|
Other disorders of intestinal carbohydrate absorption
E74.31|
Sucrase-isomaltase deficiency
E74.39|
Other disorders of intestinal carbohydrate absorption
E74.4|
Disorders of pyruvate metabolism and gluconeogenesis
E74.8|
Other specified disorders of carbohydrate metabolism
E74.81|
Disorders of glucose transport, not elsewhere classified
E74.810|
Glucose transporter protein type 1 deficiency
E74.818|
Other disorders of glucose transport
E74.819|
Disorders of glucose transport, unspecified
E74.82|
Disorders of citrate metabolism
E74.820|
SLC13A5 Citrate Transporter Disorder
E74.829|
Other disorders of citrate metabolism
E74.89|
Other specified disorders of carbohydrate metabolism
E74.9|
Disorder of carbohydrate metabolism, unspecified
E75|
Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0|
GM2 gangliosidosis
E75.00|
GM2 gangliosidosis, unspecified
E75.01|
Sandhoff disease
E75.02|
Tay-Sachs disease
E75.09|
Other GM2 gangliosidosis
E75.1|
Other and unspecified gangliosidosis
E75.10|
Unspecified gangliosidosis
E75.11|
Mucolipidosis IV

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