All ICD10 Codes
Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All CodesBillable Only
Internal Codes
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  • E72.8—

    Other specified disorders of amino-acid metabolism

  • E72.81—

    Disorders of gamma aminobutyric acid metabolism

  • E72.89—

    Other specified disorders of amino-acid metabolism

  • E72.9—

    Disorder of amino-acid metabolism, unspecified

  • E73—

    Lactose intolerance

  • E73.0—

    Congenital lactase deficiency

  • E73.1—

    Secondary lactase deficiency

  • E73.8—

    Other lactose intolerance

  • E73.9—

    Lactose intolerance, unspecified

  • E74—

    Other disorders of carbohydrate metabolism

  • E74.0—

    Glycogen storage disease

  • E74.00—

    Glycogen storage disease, unspecified

  • E74.01—

    von Gierke disease

  • E74.02—

    Pompe disease

  • E74.03—

    Cori disease

  • E74.04—

    McArdle disease

  • E74.05—

    Lysosome-associated membrane protein 2 [LAMP2] deficiency

  • E74.09—

    Other glycogen storage disease

  • E74.1—

    Disorders of fructose metabolism

  • E74.10—

    Disorder of fructose metabolism, unspecified

  • E74.11—

    Essential fructosuria

  • E74.12—

    Hereditary fructose intolerance

  • E74.19—

    Other disorders of fructose metabolism

  • E74.2—

    Disorders of galactose metabolism

  • E74.20—

    Disorders of galactose metabolism, unspecified

  • E74.21—

    Galactosemia

  • E74.29—

    Other disorders of galactose metabolism

  • E74.3—

    Other disorders of intestinal carbohydrate absorption

  • E74.31—

    Sucrase-isomaltase deficiency

  • E74.39—

    Other disorders of intestinal carbohydrate absorption

  • E74.4—

    Disorders of pyruvate metabolism and gluconeogenesis

  • E74.8—

    Other specified disorders of carbohydrate metabolism

  • E74.81—

    Disorders of glucose transport, not elsewhere classified

  • E74.810—

    Glucose transporter protein type 1 deficiency

  • E74.818—

    Other disorders of glucose transport

  • E74.819—

    Disorders of glucose transport, unspecified

  • E74.82—

    Disorders of citrate metabolism

  • E74.820—

    SLC13A5 Citrate Transporter Disorder

  • E74.829—

    Other disorders of citrate metabolism

  • E74.89—

    Other specified disorders of carbohydrate metabolism

  • E74.9—

    Disorder of carbohydrate metabolism, unspecified

  • E75—

    Disorders of sphingolipid metabolism and other lipid storage disorders

  • E75.0—

    GM2 gangliosidosis

  • E75.00—

    GM2 gangliosidosis, unspecified

  • E75.01—

    Sandhoff disease

  • E75.02—

    Tay-Sachs disease

  • E75.09—

    Other GM2 gangliosidosis

  • E75.1—

    Other and unspecified gangliosidosis

  • E75.10—

    Unspecified gangliosidosis

  • E75.11—

    Mucolipidosis IV

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