All ICD10 Codes

E74.02

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Pompe disease

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Cardiac glycogenosis
  • Type II glycogen storage disease
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E74 Notes

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E74Other disorders of carbohydrate metabolism
E74.0Glycogen storage disease
E74.02Pompe diseaseBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E74.02:

categoryE74
Other disorders of carbohydrate metabolism
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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