All ICD10 Codes

E75

Non-Billable
ChapterE00–E89
Rankcategory
Official Description

Disorders of sphingolipid metabolism and other lipid storage disorders

Use a more specific code (4 billable, 3 non-billable)
E75.0GM2 gangliosidosishas subcodesE75.1Other and unspecified gangliosidosishas subcodesE75.2Other sphingolipidosishas subcodesE75.3Sphingolipidosis, unspecifiedE75.4Neuronal ceroid lipofuscinosisE75.5Other lipid storage disordersE75.6Lipid storage disorder, unspecified
Metadata & Insights
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Instructional Notes

Excludes1(Not coded here. Use a different code.)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E75Disorders of sphingolipid metabolism and other lipid storage disordersNot billable
E75.0GM2 gangliosidosisSubcodes
E75.1Other and unspecified gangliosidosisSubcodes
E75.2Other sphingolipidosisSubcodes
E75.3Sphingolipidosis, unspecifiedBillable
E75.4Neuronal ceroid lipofuscinosisBillable
E75.5Other lipid storage disordersBillable
E75.6Lipid storage disorder, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E75:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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