E75.240

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Niemann-Pick disease type A

Metadata & Insights
  • Billable/specific code (valid for reimbursement).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Acid sphingomyelinase deficiency type A (ASMD type A)
  • Infantile neurovisceral acid sphingomyelinase deficiency
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E75Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2Other sphingolipidosis
E75.24Niemann-Pick disease
E75.240Niemann-Pick disease type ABillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E75.240:

subcategoryE75.24
Niemann-Pick disease
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subcategoryE75.2
Other sphingolipidosis
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categoryE75
Disorders of sphingolipid metabolism and other lipid storage disorders
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blockE70-E88
Metabolic disorders (E70-E88)
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chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
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MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

Cross Reference

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