All ICD10 Codes

E75.244

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Niemann-Pick disease type A/B

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
  • Chronic neurovisceral acid sphingomyelinase deficiency
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E75 NotesView E75.2 NotesView E75.24 Notes

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E75Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2Other sphingolipidosis
E75.24Niemann-Pick disease
E75.244Niemann-Pick disease type A/BBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E75.244:

subcategoryE75.24
Niemann-Pick disease
View context instructions
subcategoryE75.2
Other sphingolipidosis
View context instructions
categoryE75
Disorders of sphingolipid metabolism and other lipid storage disorders
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Code History

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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