HCC 49 (V28)
Specified Lysosomal Storage Disorders
13 ICD-10-CM codes map to this category in the CMS-HCC V28 risk adjustment model for payment year 2027. All 115 HCCs
| E74.02 | Pompe disease |
| E75.21 | Fabry (-Anderson) disease |
| E75.22 | Gaucher disease |
| E76.01 | Hurler's syndrome |
| E76.02 | Hurler-Scheie syndrome |
| E76.03 | Scheie's syndrome |
| E76.1 | Mucopolysaccharidosis, type II |
| E76.210 | Morquio A mucopolysaccharidoses |
| E76.211 | Morquio B mucopolysaccharidoses |
| E76.219 | Morquio mucopolysaccharidoses, unspecified |
| E76.22 | Sanfilippo mucopolysaccharidoses |
| E76.29 | Other mucopolysaccharidoses |
| E76.3 | Mucopolysaccharidosis, unspecified |
