HCC 49 (V28)

Specified Lysosomal Storage Disorders

13 ICD-10-CM codes map to this category in the CMS-HCC V28 risk adjustment model for payment year 2027. All 115 HCCs

E74.02Pompe disease
E75.21Fabry (-Anderson) disease
E75.22Gaucher disease
E76.01Hurler's syndrome
E76.02Hurler-Scheie syndrome
E76.03Scheie's syndrome
E76.1Mucopolysaccharidosis, type II
E76.210Morquio A mucopolysaccharidoses
E76.211Morquio B mucopolysaccharidoses
E76.219Morquio mucopolysaccharidoses, unspecified
E76.22Sanfilippo mucopolysaccharidoses
E76.29Other mucopolysaccharidoses
E76.3Mucopolysaccharidosis, unspecified