All ICD10 Codes
Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All CodesBillable Only
Internal Codes
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  • E70.33|

    Albinism with hematologic abnormality

  • E70.330|

    Chediak-Higashi syndrome

  • E70.331|

    Hermansky-Pudlak syndrome

  • E70.338|

    Other albinism with hematologic abnormality

  • E70.339|

    Albinism with hematologic abnormality, unspecified

  • E70.39|

    Other specified albinism

  • E70.4|

    Disorders of histidine metabolism

  • E70.40|

    Disorders of histidine metabolism, unspecified

  • E70.41|

    Histidinemia

  • E70.49|

    Other disorders of histidine metabolism

  • E70.5|

    Disorders of tryptophan metabolism

  • E70.8|

    Other disorders of aromatic amino-acid metabolism

  • E70.81|

    Aromatic L-amino acid decarboxylase deficiency

  • E70.89|

    Other disorders of aromatic amino-acid metabolism

  • E70.9|

    Disorder of aromatic amino-acid metabolism, unspecified

  • E71|

    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

  • E71.0|

    Maple-syrup-urine disease

  • E71.1|

    Other disorders of branched-chain amino-acid metabolism

  • E71.11|

    Branched-chain organic acidurias

  • E71.110|

    Isovaleric acidemia

  • E71.111|

    3-methylglutaconic aciduria

  • E71.118|

    Other branched-chain organic acidurias

  • E71.12|

    Disorders of propionate metabolism

  • E71.120|

    Methylmalonic acidemia

  • E71.121|

    Propionic acidemia

  • E71.128|

    Other disorders of propionate metabolism

  • E71.19|

    Other disorders of branched-chain amino-acid metabolism

  • E71.2|

    Disorder of branched-chain amino-acid metabolism, unspecified

  • E71.3|

    Disorders of fatty-acid metabolism

  • E71.30|

    Disorder of fatty-acid metabolism, unspecified

  • E71.31|

    Disorders of fatty-acid oxidation

  • E71.310|

    Long chain/very long chain acyl CoA dehydrogenase deficiency

  • E71.311|

    Medium chain acyl CoA dehydrogenase deficiency

  • E71.312|

    Short chain acyl CoA dehydrogenase deficiency

  • E71.313|

    Glutaric aciduria type II

  • E71.314|

    Muscle carnitine palmitoyltransferase deficiency

  • E71.318|

    Other disorders of fatty-acid oxidation

  • E71.32|

    Disorders of ketone metabolism

  • E71.39|

    Other disorders of fatty-acid metabolism

  • E71.4|

    Disorders of carnitine metabolism

  • E71.40|

    Disorder of carnitine metabolism, unspecified

  • E71.41|

    Primary carnitine deficiency

  • E71.42|

    Carnitine deficiency due to inborn errors of metabolism

  • E71.43|

    Iatrogenic carnitine deficiency

  • E71.44|

    Other secondary carnitine deficiency

  • E71.440|

    Ruvalcaba-Myhre-Smith syndrome

  • E71.448|

    Other secondary carnitine deficiency

  • E71.5|

    Peroxisomal disorders

  • E71.50|

    Peroxisomal disorder, unspecified

  • E71.51|

    Disorders of peroxisome biogenesis

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