E00–E89: Endocrine, Nutritional and Metabolic Diseases
Chapter 4 of ICD-10-CM 2027, 1,270 codes in 10 blocks.
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Chapter instructions
Excludes1: not coded here, use a different code
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Codes in this chapter
All codesBillable only1,270 results
- E70.33Albinism with hematologic abnormality
- E70.330Chediak-Higashi syndrome
- E70.331Hermansky-Pudlak syndrome
- E70.338Other albinism with hematologic abnormality
- E70.339Albinism with hematologic abnormality, unspecified
- E70.39Other specified albinism
- E70.4Disorders of histidine metabolism
- E70.40Disorders of histidine metabolism, unspecified
- E70.41Histidinemia
- E70.49Other disorders of histidine metabolism
- E70.5Disorders of tryptophan metabolism
- E70.8Other disorders of aromatic amino-acid metabolism
- E70.81Aromatic L-amino acid decarboxylase deficiency
- E70.89Other disorders of aromatic amino-acid metabolism
- E70.9Disorder of aromatic amino-acid metabolism, unspecified
- E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
- E71.0Maple-syrup-urine disease
- E71.1Other disorders of branched-chain amino-acid metabolism
- E71.11Branched-chain organic acidurias
- E71.110Isovaleric acidemia
- E71.1113-methylglutaconic aciduria
- E71.118Other branched-chain organic acidurias
- E71.12Disorders of propionate metabolism
- E71.120Methylmalonic acidemia
- E71.121Propionic acidemia
- E71.128Other disorders of propionate metabolism
- E71.19Other disorders of branched-chain amino-acid metabolism
- E71.2Disorder of branched-chain amino-acid metabolism, unspecified
- E71.3Disorders of fatty-acid metabolism
- E71.30Disorder of fatty-acid metabolism, unspecified
- E71.31Disorders of fatty-acid oxidation
- E71.310Long chain/very long chain acyl CoA dehydrogenase deficiency
- E71.311Medium chain acyl CoA dehydrogenase deficiency
- E71.312Short chain acyl CoA dehydrogenase deficiency
- E71.313Glutaric aciduria type II
- E71.314Muscle carnitine palmitoyltransferase deficiency
- E71.318Other disorders of fatty-acid oxidation
- E71.32Disorders of ketone metabolism
- E71.39Other disorders of fatty-acid metabolism
- E71.4Disorders of carnitine metabolism
- E71.40Disorder of carnitine metabolism, unspecified
- E71.41Primary carnitine deficiency
- E71.42Carnitine deficiency due to inborn errors of metabolism
- E71.43Iatrogenic carnitine deficiency
- E71.44Other secondary carnitine deficiency
- E71.440Ruvalcaba-Myhre-Smith syndrome
- E71.448Other secondary carnitine deficiency
- E71.5Peroxisomal disorders
- E71.50Peroxisomal disorder, unspecified
- E71.51Disorders of peroxisome biogenesis
