E71.3

Non-Billable
ChapterE00–E89
Ranksubcategory
Official Description

Disorders of fatty-acid metabolism

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Excludes1(Not coded here. Use a different code.)
  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)
Excludes2(Not included here. Code separately if applicable.)
  • carnitine deficiency due to inborn error of metabolism (E71.42)
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.3Disorders of fatty-acid metabolismNot billable
E71.30Disorder of fatty-acid metabolism, unspecifiedBillable
E71.31Disorders of fatty-acid oxidationSubcodes
E71.32Disorders of ketone metabolismBillable
E71.39Other disorders of fatty-acid metabolismBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E71.3:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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