All ICD10 Codes
E71Non-billable

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Endocrine, Nutritional and Metabolic Diseases·Metabolic disorders (E70-E88)·category·FY 2026

Use a more specific code (2 billable, 4 non-billable)
E71.0Maple-syrup-urine diseaseE71.1Other disorders of branched-chain amino-acid metabolismhas subcodesE71.2Disorder of branched-chain amino-acid metabolism, unspecifiedE71.3Disorders of fatty-acid metabolismhas subcodesE71.4Disorders of carnitine metabolismhas subcodesE71.5Peroxisomal disordershas subcodes

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolismNot billable
E71.0Maple-syrup-urine diseaseBillable
E71.1Other disorders of branched-chain amino-acid metabolismSubcodes
E71.2Disorder of branched-chain amino-acid metabolism, unspecifiedBillable
E71.3Disorders of fatty-acid metabolismSubcodes
E71.4Disorders of carnitine metabolismSubcodes
E71.5Peroxisomal disordersSubcodes

MS-DRG Classification

2026

No direct MS-DRG triggers identified.