E71.4

Non-Billable
ChapterE00–E89
Ranksubcategory
Official Description

Disorders of carnitine metabolism

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Excludes1(Not coded here. Use a different code.)
  • Muscle carnitine palmitoyltransferase deficiency (E71.314)
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.4Disorders of carnitine metabolismNot billable
E71.40Disorder of carnitine metabolism, unspecifiedBillable
E71.41Primary carnitine deficiencyBillable
E71.42Carnitine deficiency due to inborn errors of metabolismBillable
E71.43Iatrogenic carnitine deficiencyBillable
E71.44Other secondary carnitine deficiencySubcodes

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E71.4:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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