E72.2

Non-Billable
ChapterE00–E89
Ranksubcategory
Official Description

Disorders of urea cycle metabolism

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Excludes1(Not coded here. Use a different code.)
  • disorders of ornithine metabolism (E72.4)
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E72Other disorders of amino-acid metabolism
E72.2Disorders of urea cycle metabolismNot billable
E72.20Disorder of urea cycle metabolism, unspecifiedBillable
E72.21ArgininemiaBillable
E72.22Arginosuccinic aciduriaBillable
E72.23CitrullinemiaBillable
E72.29Other disorders of urea cycle metabolismBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E72.2:

categoryE72
Other disorders of amino-acid metabolism
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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