E72

Non-Billable
ChapterE00–E89
Rankcategory
Official Description

Other disorders of amino-acid metabolism

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Instructional Notes

Excludes1(Not coded here. Use a different code.)
  • disorders of:
  • aromatic amino-acid metabolism (E70.-)
  • branched-chain amino-acid metabolism (E71.0-E71.2)
  • fatty-acid metabolism (E71.3)
  • purine and pyrimidine metabolism (E79.-)
  • gout (M1A.-, M10.-)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E72Other disorders of amino-acid metabolismNot billable
E72.0Disorders of amino-acid transportSubcodes
E72.1Disorders of sulfur-bearing amino-acid metabolismSubcodes
E72.2Disorders of urea cycle metabolismSubcodes
E72.3Disorders of lysine and hydroxylysine metabolismBillable
E72.4Disorders of ornithine metabolismBillable
E72.5Disorders of glycine metabolismSubcodes
E72.8Other specified disorders of amino-acid metabolismSubcodes
E72.9Disorder of amino-acid metabolism, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E72:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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