Disorders of aromatic amino-acid metabolism
In Metabolic disorders (E70-E88), chapter 4: Endocrine, Nutritional and Metabolic Diseases
26 billable codes under E70: all are a CC; none map to an HCC.A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment.
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Instructional notes
Also applies, from Metabolic disorders (E70-E88)
These notes sit on E70-E88 and apply to every code under it, including E70.
Excludes1: not coded here, use a different code
Excludes2: not included here, code separately if applicable
- Ehlers-Danlos syndromes (Q79.6-)
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers diabetes mellitus coding, including type, insulin and drug use, pump malfunction and secondary diabetes, plus obesity and obesity class codes.
- Diabetes mellitus (page 39)
- Obesity (page 42)
All codes under E70
E70 can't be used on a claim. Pick a billable code below; grey headings group them.
- E70.0Classical phenylketonuria
- E70.1Other hyperphenylalaninemias
- E70.2Disorders of tyrosine metabolism
- E70.20Disorder of tyrosine metabolism, unspecified
- E70.21Tyrosinemia
- E70.29Other disorders of tyrosine metabolism
- E70.3Albinism
- E70.30Albinism, unspecified
- E70.31Ocular albinism
- E70.310X-linked ocular albinism
- E70.311Autosomal recessive ocular albinism
- E70.318Other ocular albinism
- E70.319Ocular albinism, unspecified
- E70.32Oculocutaneous albinism
- E70.320Tyrosinase negative oculocutaneous albinism
- E70.321Tyrosinase positive oculocutaneous albinism
- E70.328Other oculocutaneous albinism
- E70.329Oculocutaneous albinism, unspecified
- E70.33Albinism with hematologic abnormality
- E70.330Chediak-Higashi syndrome
- E70.331Hermansky-Pudlak syndrome
- E70.338Other albinism with hematologic abnormality
- E70.339Albinism with hematologic abnormality, unspecified
- E70.39Other specified albinism
- E70.4Disorders of histidine metabolism
- E70.40Disorders of histidine metabolism, unspecified
- E70.41Histidinemia
- E70.49Other disorders of histidine metabolism
- E70.5Disorders of tryptophan metabolism
- E70.8Other disorders of aromatic amino-acid metabolism
- E70.81Aromatic L-amino acid decarboxylase deficiency
- E70.89Other disorders of aromatic amino-acid metabolism
- E70.9Disorder of aromatic amino-acid metabolism, unspecified
E70 MS-DRG
As the principal diagnosis, all 26 billable codes under E70 group to MS-DRG 642 (v44.0).
Other codes that refer to E70
Notes on these codes point to E70.
- CH17 Excludes2: inborn errors of metabolism (E70-E88)
- E72 Excludes1: aromatic amino-acid metabolism (E70.-)
- G11 Excludes2: metabolic disorders (E70-E88)
- G63 Code First: metabolic diseases (E70-E88)
- G71 Excludes2: metabolic disorders (E70-E88)
- H42 Code First: specified metabolic disorder (E70-E88)
- N25.0 Excludes2: metabolic disorders classifiable to E70-E88
- N25.81 Excludes2: metabolic disorders classifiable to E70-E88
- P59 Excludes1: jaundice due to inborn errors of metabolism (E70-E88)
- R79 Excludes1: specific findings indicating disorder of amino-acid metabolism (E70-E72)
- R79.83 Excludes1: disorders of amino-acid metabolism (E70-E72)
- R80-R82 Excludes1: specific findings indicating disorder of amino-acid metabolism (E70-E72)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Metabolic Disorders
Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.
Read more about metabolic disorders on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
