E70

Non-Billable
ChapterE00–E89
Rankcategory
Official Description

Disorders of aromatic amino-acid metabolism

Metadata & Insights
  • Non-billable category (requires more specific sub-code).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E70Disorders of aromatic amino-acid metabolismNot billable
E70.0Classical phenylketonuriaBillable
E70.1Other hyperphenylalaninemiasBillable
E70.2Disorders of tyrosine metabolismSubcodes
E70.3AlbinismSubcodes
E70.4Disorders of histidine metabolismSubcodes
E70.5Disorders of tryptophan metabolismBillable
E70.8Other disorders of aromatic amino-acid metabolismSubcodes
E70.9Disorder of aromatic amino-acid metabolism, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E70:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

Find Procedures (ICD-10-PCS)

Find surgical and procedural codes related to Disorders of aromatic amino-acid metabolism.

Search PCS Codes