Other congenital malformations, not elsewhere classified
In Other congenital malformations (Q80-Q89), chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
10 billable codes under Q89: 1 is an MCC, 6 are a CC; none map to an HCC.A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment.
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Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q89
Q89 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q89.0Congenital absence and malformations of spleen
- Q89.01Asplenia (congenital)
- Q89.09Congenital malformations of spleen
- Q89.1Congenital malformations of adrenal gland
- Q89.2Congenital malformations of other endocrine glands
- Q89.3Situs inversus
- Q89.4Conjoined twins
- Q89.7Multiple congenital malformations, not elsewhere classified
- Q89.8Other specified congenital malformations
- Q89.81Kabuki syndrome
- Q89.89Other specified congenital malformations
- Q89.9Congenital malformation, unspecified
Q89 MS-DRGs
As the principal diagnosis, the billable codes under Q89 group to these 15 MS-DRGs (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 564 Other Musculoskeletal System and Connective Tissue Diagnoses with MCC (3 of 10 codes)
- DRG 565 Other Musculoskeletal System and Connective Tissue Diagnoses with CC (3 of 10 codes)
- DRG 566 Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC (3 of 10 codes)
- DRG 393 Other Digestive System Diagnoses with MCC (2 of 10 codes)
- DRG 394 Other Digestive System Diagnoses with CC (2 of 10 codes)
- DRG 395 Other Digestive System Diagnoses without CC/MCC (2 of 10 codes)
- DRG 643 Endocrine Disorders with MCC (2 of 10 codes)
- DRG 644 Endocrine Disorders with CC (2 of 10 codes)
- DRG 645 Endocrine Disorders without CC/MCC (2 of 10 codes)
- DRG 814 Reticuloendothelial and Immunity Disorders with MCC (2 of 10 codes)
- DRG 815 Reticuloendothelial and Immunity Disorders with CC (2 of 10 codes)
- DRG 816 Reticuloendothelial and Immunity Disorders without CC/MCC (2 of 10 codes)
- DRG 791 Prematurity with Major Problems (1 of 10 codes)
- DRG 793 Full Term Neonate with Major Problems (1 of 10 codes)
- DRG 951 Other Factors Influencing Health Status (1 of 10 codes)
Other codes that refer to Q89
Notes on these codes point to Q89.
- Z87.7 Includes: Conditions classifiable to Q00-Q89 that have been repaired or corrected
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
Read more about birth defects on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
