Q80-Q89Not billable, use a more specific code below
Other congenital malformations (Q80-Q89)
chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
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Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q80-Q89
Q80-Q89 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q80Congenital ichthyosis
- Q80.0Ichthyosis vulgaris
- Q80.1X-linked ichthyosis
- Q80.2Lamellar ichthyosis
- Q80.3Congenital bullous ichthyosiform erythroderma
- Q80.4Harlequin fetus
- Q80.8Other congenital ichthyosis
- Q80.9Congenital ichthyosis, unspecified
- Q81Epidermolysis bullosa
- Q81.0Epidermolysis bullosa simplex
- Q81.1Epidermolysis bullosa letalis
- Q81.2Epidermolysis bullosa dystrophica
- Q81.8Other epidermolysis bullosa
- Q81.9Epidermolysis bullosa, unspecified
- Q82Other congenital malformations of skin
- Q82.0Hereditary lymphedema
- Q82.1Xeroderma pigmentosum
- Q82.2Congenital cutaneous mastocytosis
- Q82.3Incontinentia pigmenti
- Q82.4Ectodermal dysplasia (anhidrotic)
- Q82.5Congenital non-neoplastic nevus
- Q82.6Congenital sacral dimple
- Q82.8Other specified congenital malformations of skin
- Q82.9Congenital malformation of skin, unspecified
- Q83Congenital malformations of breast
- Q83.0Congenital absence of breast with absent nipple
- Q83.1Accessory breast
- Q83.2Absent nipple
- Q83.3Accessory nipple
- Q83.8Other congenital malformations of breast
- Q83.9Congenital malformation of breast, unspecified
- Q84Other congenital malformations of integument
- Q84.0Congenital alopecia
- Q84.1Congenital morphological disturbances of hair, not elsewhere classified
- Q84.2Other congenital malformations of hair
- Q84.3Anonychia
- Q84.4Congenital leukonychia
- Q84.5Enlarged and hypertrophic nails
- Q84.6Other congenital malformations of nails
- Q84.8Other specified congenital malformations of integument
- Q84.9Congenital malformation of integument, unspecified
- Q85Phakomatoses, not elsewhere classified
- Q85.0Neurofibromatosis (nonmalignant)
- Q85.00Neurofibromatosis, unspecified
- Q85.01Neurofibromatosis, type 1
- Q85.02Neurofibromatosis, type 2
- Q85.03Schwannomatosis
- Q85.09Other neurofibromatosis
- Q85.1Tuberous sclerosis
- Q85.8Other phakomatoses, not elsewhere classified
- Q85.81PTEN hamartoma tumor syndrome
- Q85.82Other Cowden syndrome
- Q85.83Von Hippel-Lindau syndrome
- Q85.89Other phakomatoses, not elsewhere classified
- Q85.9Phakomatosis, unspecified
- Q86Congenital malformation syndromes due to known exogenous causes, not elsewhere classified
- Q86.0Fetal alcohol syndrome (dysmorphic)
- Q86.1Fetal hydantoin syndrome
- Q86.2Dysmorphism due to warfarin
- Q86.8Other congenital malformation syndromes due to known exogenous causes
- Q87Other specified congenital malformation syndromes affecting multiple systems
- Q87.0Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1Congenital malformation syndromes predominantly associated with short stature
- Q87.11Prader-Willi syndrome
- Q87.19Other congenital malformation syndromes predominantly associated with short stature
- Q87.2Congenital malformation syndromes predominantly involving limbs
- Q87.3Congenital malformation syndromes involving early overgrowth
- Q87.4Marfan syndrome
- Q87.40Marfan syndrome, unspecified
- Q87.41Marfan syndrome with cardiovascular manifestations
- Q87.410Marfan syndrome with aortic dilation
- Q87.418Marfan syndrome with other cardiovascular manifestations
- Q87.42Marfan syndrome with ocular manifestations
- Q87.43Marfan syndrome with skeletal manifestation
- Q87.5Other congenital malformation syndromes with other skeletal changes
- Q87.8Other specified congenital malformation syndromes, not elsewhere classified
- Q87.81Alport syndrome
- Q87.82Arterial tortuosity syndrome
- Q87.83Bardet-Biedl syndrome
- Q87.84Laurence-Moon syndrome
- Q87.85MED13L syndrome
- Q87.86Kleefstra syndrome
- Q87.87Hao-Fountain Syndrome
- Q87.88CTNNB1 syndrome
- Q87.89Other specified congenital malformation syndromes, not elsewhere classified
- Q87.ALoeys-Dietz syndrome
- Q89Other congenital malformations, not elsewhere classified
- Q89.0Congenital absence and malformations of spleen
- Q89.01Asplenia (congenital)
- Q89.09Congenital malformations of spleen
- Q89.1Congenital malformations of adrenal gland
- Q89.2Congenital malformations of other endocrine glands
- Q89.3Situs inversus
- Q89.4Conjoined twins
- Q89.7Multiple congenital malformations, not elsewhere classified
- Q89.8Other specified congenital malformations
- Q89.81Kabuki syndrome
- Q89.89Other specified congenital malformations
- Q89.9Congenital malformation, unspecified
Q80-Q89 MS-DRGs
This code does not group to an MS-DRG as a principal diagnosis.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
Read more about skin conditions on MedlinePlus