All ICD10 Codes

Q85.89

Billable
ChapterQ00–Q99
Ranksubcategory
Official Description

Other phakomatoses, not elsewhere classified

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes
  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome
General instructions are available for the parent sections:
View CH17 NotesView Q85 NotesView Q85.8 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q80-Q89Other congenital malformations (Q80-Q89)
Q85Phakomatoses, not elsewhere classified
Q85.8Other phakomatoses, not elsewhere classified
Q85.89Other phakomatoses, not elsewhere classified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q85.89:

subcategoryQ85.8
Other phakomatoses, not elsewhere classified
View context instructions
categoryQ85
Phakomatoses, not elsewhere classified
View context instructions
chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q85.89. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

8 raw paths
Angiomatosis1 unique routes
encephalotrigeminal→Q85.89
Dimitri-Sturge-Weber disease1 unique routes
Direct index entry→Q85.89
Kraft-Weber-Dimitri disease1 unique routes
Direct index entry→Q85.89
Peutz-Jeghers disease or syndrome1 unique routes
Direct index entry→Q85.89
Phakomatosis1 unique routes
specified NEC→Q85.89
Sturge (-Weber) (-Dimitri) (-Kalischer) disease or syndrome1 unique routes
Direct index entry→Q85.89
Syndrome2 unique routes
Peutz-Jeghers→Q85.89
Sturge-Weber (-Dimitri)→Q85.89

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 826
Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with MCC
DRG 827
Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with CC
DRG 828
Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures without CC/MCC
DRG 829
Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures with CC/MCC
DRG 830
Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures without CC/MCC
DRG 843
Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with MCC
DRG 844
Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with CC
DRG 845
Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses without CC/MCC

Cross Reference

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