Phakomatoses, not elsewhere classified
In Other congenital malformations (Q80-Q89), chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
11 billable codes under Q85: 6 are a CC; all map to HCC 23 (Prostate, Breast, and Other Cancers and Tumors).A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment. An HCC counts toward a Medicare Advantage patient's risk score.
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Instructional notes
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q85
Q85 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q85.0Neurofibromatosis (nonmalignant)
- Q85.00Neurofibromatosis, unspecified
- Q85.01Neurofibromatosis, type 1
- Q85.02Neurofibromatosis, type 2
- Q85.03Schwannomatosis
- Q85.09Other neurofibromatosis
- Q85.1Tuberous sclerosis
- Q85.8Other phakomatoses, not elsewhere classified
- Q85.81PTEN hamartoma tumor syndrome
- Q85.82Other Cowden syndrome
- Q85.83Von Hippel-Lindau syndrome
- Q85.89Other phakomatoses, not elsewhere classified
- Q85.9Phakomatosis, unspecified
Q85 MS-DRGs
As the principal diagnosis, the billable codes under Q85 group to these 11 MS-DRGs (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 091 Other Disorders of Nervous System with MCC (6 of 11 codes)
- DRG 092 Other Disorders of Nervous System with CC (6 of 11 codes)
- DRG 093 Other Disorders of Nervous System without CC/MCC (6 of 11 codes)
- DRG 826 Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with MCC (5 of 11 codes)
- DRG 827 Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with CC (5 of 11 codes)
- DRG 828 Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures without CC/MCC (5 of 11 codes)
- DRG 829 Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures with CC/MCC (5 of 11 codes)
- DRG 830 Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures without CC/MCC (5 of 11 codes)
- DRG 843 Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with MCC (5 of 11 codes)
- DRG 844 Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with CC (5 of 11 codes)
- DRG 845 Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses without CC/MCC (5 of 11 codes)
Code history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
