All ICD10 Codes
Chapter 3

D50–D89: Diseases of the Blood and Blood-Forming Organs

Diseases of the Blood and Blood-Forming Organs diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
All CodesBillable Only
Internal Codes
PrevNext
  • D81.0—

    Severe combined immunodeficiency [SCID] with reticular dysgenesis

  • D81.1—

    Severe combined immunodeficiency [SCID] with low T- and B-cell numbers

  • D81.2—

    Severe combined immunodeficiency [SCID] with low or normal B-cell numbers

  • D81.30—

    Adenosine deaminase deficiency, unspecified

  • D81.31—

    Severe combined immunodeficiency due to adenosine deaminase deficiency

  • D81.32—

    Adenosine deaminase 2 deficiency

  • D81.39—

    Other adenosine deaminase deficiency

  • D81.4—

    Nezelof's syndrome

  • D81.5—

    Purine nucleoside phosphorylase [PNP] deficiency

  • D81.6—

    Major histocompatibility complex class I deficiency

  • D81.7—

    Major histocompatibility complex class II deficiency

  • D81.810—

    Biotinidase deficiency

  • D81.818—

    Other biotin-dependent carboxylase deficiency

  • D81.819—

    Biotin-dependent carboxylase deficiency, unspecified

  • D81.82—

    Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]

  • D81.89—

    Other combined immunodeficiencies

  • D81.9—

    Combined immunodeficiency, unspecified

  • D82.0—

    Wiskott-Aldrich syndrome

  • D82.1—

    Di George's syndrome

  • D82.2—

    Immunodeficiency with short-limbed stature

  • D82.3—

    Immunodeficiency following hereditary defective response to Epstein-Barr virus

  • D82.4—

    Hyperimmunoglobulin E [IgE] syndrome

  • D82.8—

    Immunodeficiency associated with other specified major defects

  • D82.9—

    Immunodeficiency associated with major defect, unspecified

  • D83.0—

    Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function

  • D83.1—

    Common variable immunodeficiency with predominant immunoregulatory T-cell disorders

  • D83.2—

    Common variable immunodeficiency with autoantibodies to B- or T-cells

  • D83.8—

    Other common variable immunodeficiencies

  • D83.9—

    Common variable immunodeficiency, unspecified

  • D84.0—

    Lymphocyte function antigen-1 [LFA-1] defect

  • D84.1—

    Defects in the complement system

  • D84.81—

    Immunodeficiency due to conditions classified elsewhere

  • D84.821—

    Immunodeficiency due to drugs

  • D84.822—

    Immunodeficiency due to external causes

  • D84.89—

    Other immunodeficiencies

  • D84.9—

    Immunodeficiency, unspecified

  • D86.0—

    Sarcoidosis of lung

  • D86.1—

    Sarcoidosis of lymph nodes

  • D86.2—

    Sarcoidosis of lung with sarcoidosis of lymph nodes

  • D86.3—

    Sarcoidosis of skin

  • D86.81—

    Sarcoid meningitis

  • D86.82—

    Multiple cranial nerve palsies in sarcoidosis

  • D86.83—

    Sarcoid iridocyclitis

  • D86.84—

    Sarcoid pyelonephritis

  • D86.85—

    Sarcoid myocarditis

  • D86.86—

    Sarcoid arthropathy

  • D86.87—

    Sarcoid myositis

  • D86.89—

    Sarcoidosis of other sites

  • D86.9—

    Sarcoidosis, unspecified

  • D89.0—

    Polyclonal hypergammaglobulinemia

PreviousPage 6 of 7Next