All ICD10 Codes

D81.819

Billable
ChapterD50–D89
Ranksubcategory
Official Description

Biotin-dependent carboxylase deficiency, unspecified

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Includes
  • Multiple carboxylase deficiency, unspecified
General instructions are available for the parent sections:
View CH3 NotesView D80-D89 NotesView D81 NotesView D81.81 Notes

Clinical Hierarchy

BillableHas subcodes
CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89Certain disorders involving the immune mechanism (D80-D89)
D81Combined immunodeficiencies
D81.8Other combined immunodeficiencies
D81.81Biotin-dependent carboxylase deficiency
D81.819Biotin-dependent carboxylase deficiency, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D81.819:

subcategoryD81.81
Biotin-dependent carboxylase deficiency
View context instructions
categoryD81
Combined immunodeficiencies
View context instructions
blockD80-D89
Certain disorders involving the immune mechanism (D80-D89)
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 640
Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes with MCC
DRG 641
Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes without MCC

Cross Reference

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