All ICD10 Codes

D81.81

Non-Billable
ChapterD50–D89
Ranksubcategory
Official Description

Biotin-dependent carboxylase deficiency

Use a more specific code (3 billable)
D81.810Biotinidase deficiencyD81.818Other biotin-dependent carboxylase deficiencyD81.819Biotin-dependent carboxylase deficiency, unspecified
Metadata & Insights
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Includes
  • Multiple carboxylase deficiency
Excludes1(Not coded here. Use a different code.)
  • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
General instructions are available for the parent sections:
View CH3 NotesView D80-D89 NotesView D81 Notes

Clinical Hierarchy

BillableHas subcodes
CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89Certain disorders involving the immune mechanism (D80-D89)
D81Combined immunodeficiencies
D81.8Other combined immunodeficiencies
D81.81Biotin-dependent carboxylase deficiencyNot billable
D81.810Biotinidase deficiencyBillable
D81.818Other biotin-dependent carboxylase deficiencyBillable
D81.819Biotin-dependent carboxylase deficiency, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D81.81:

categoryD81
Combined immunodeficiencies
View context instructions
blockD80-D89
Certain disorders involving the immune mechanism (D80-D89)
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

Find Procedures (ICD-10-PCS)

Find surgical and procedural codes related to Biotin-dependent carboxylase deficiency.

Search PCS Codes