M30-M36Not billable, use a more specific code below
Systemic connective tissue disorders (M30-M36)
chapter 13: Diseases of the Musculoskeletal System and Connective Tissue
Advertisements
Instructional notes
Includes: conditions that are coded here
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes1: not coded here, use a different code
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers site and laterality, acute injury versus chronic musculoskeletal conditions, 7th characters for pathologic fractures, osteoporosis with or without current fracture, and multisystem inflammatory syndrome.
- Site and laterality (page 60)
- Acute traumatic versus chronic or recurrent musculoskeletal conditions (page 61)
- Coding of Pathologic Fractures (page 61)
- Osteoporosis (page 61)
- Multisystem Inflammatory Syndrome (page 62)
All codes under M30-M36
M30-M36 can't be used on a claim. Pick a billable code below; grey headings group them.
- M30Polyarteritis nodosa and related conditions
- M30.0Polyarteritis nodosa
- M30.1Polyarteritis with lung involvement [Churg-Strauss]
- M30.2Juvenile polyarteritis
- M30.3Mucocutaneous lymph node syndrome [Kawasaki]
- M30.8Other conditions related to polyarteritis nodosa
- M31Other necrotizing vasculopathies
- M31.0Hypersensitivity angiitis
- M31.1Thrombotic microangiopathy
- M31.10Thrombotic microangiopathy, unspecified
- M31.11Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
- M31.19Other thrombotic microangiopathy
- M31.2Lethal midline granuloma
- M31.3Wegener's granulomatosis
- M31.30Wegener's granulomatosis without renal involvement
- M31.31Wegener's granulomatosis with renal involvement
- M31.4Aortic arch syndrome [Takayasu]
- M31.5Giant cell arteritis with polymyalgia rheumatica
- M31.6Other giant cell arteritis
- M31.7Microscopic polyangiitis
- M31.8Other specified necrotizing vasculopathies
- M31.9Necrotizing vasculopathy, unspecified
- M32Systemic lupus erythematosus (SLE)
- M32.0Drug-induced systemic lupus erythematosus
- M32.1Systemic lupus erythematosus with organ or system involvement
- M32.10Systemic lupus erythematosus, organ or system involvement unspecified
- M32.11Endocarditis in systemic lupus erythematosus
- M32.12Pericarditis in systemic lupus erythematosus
- M32.13Lung involvement in systemic lupus erythematosus
- M32.14Glomerular disease in systemic lupus erythematosus
- M32.15Tubulo-interstitial nephropathy in systemic lupus erythematosus
- M32.19Other organ or system involvement in systemic lupus erythematosus
- M32.8Other forms of systemic lupus erythematosus
- M32.9Systemic lupus erythematosus, unspecified
- M33Dermatopolymyositis
- M33.0Juvenile dermatomyositis
- M33.00Juvenile dermatomyositis, organ involvement unspecified
- M33.01Juvenile dermatomyositis with respiratory involvement
- M33.02Juvenile dermatomyositis with myopathy
- M33.03Juvenile dermatomyositis without myopathy
- M33.09Juvenile dermatomyositis with other organ involvement
- M33.1Other dermatomyositis
- M33.10Other dermatomyositis, organ involvement unspecified
- M33.11Other dermatomyositis with respiratory involvement
- M33.12Other dermatomyositis with myopathy
- M33.13Other dermatomyositis without myopathy
- M33.19Other dermatomyositis with other organ involvement
- M33.2Polymyositis
- M33.20Polymyositis, organ involvement unspecified
- M33.21Polymyositis with respiratory involvement
- M33.22Polymyositis with myopathy
- M33.29Polymyositis with other organ involvement
- M33.9Dermatopolymyositis, unspecified
- M33.90Dermatopolymyositis, unspecified, organ involvement unspecified
- M33.91Dermatopolymyositis, unspecified with respiratory involvement
- M33.92Dermatopolymyositis, unspecified with myopathy
- M33.93Dermatopolymyositis, unspecified without myopathy
- M33.99Dermatopolymyositis, unspecified with other organ involvement
- M34Systemic sclerosis [scleroderma]
- M34.0Progressive systemic sclerosis
- M34.1CR(E)ST syndrome
- M34.2Systemic sclerosis induced by drug and chemical
- M34.8Other forms of systemic sclerosis
- M34.81Systemic sclerosis with lung involvement
- M34.82Systemic sclerosis with myopathy
- M34.83Systemic sclerosis with polyneuropathy
- M34.89Other systemic sclerosis
- M34.9Systemic sclerosis, unspecified
- M35Other systemic involvement of connective tissue
- M35.0Sjögren syndrome
- M35.00Sjogren syndrome, unspecified
- M35.01Sjogren syndrome with keratoconjunctivitis
- M35.02Sjogren syndrome with lung involvement
- M35.03Sjogren syndrome with myopathy
- M35.04Sjogren syndrome with tubulo-interstitial nephropathy
- M35.05Sjogren syndrome with inflammatory arthritis
- M35.06Sjogren syndrome with peripheral nervous system involvement
- M35.07Sjogren syndrome with central nervous system involvement
- M35.08Sjogren syndrome with gastrointestinal involvement
- M35.09Sjogren syndrome with other organ involvement
- M35.0ASjogren syndrome with glomerular disease
- M35.0BSjogren syndrome with vasculitis
- M35.0CSjogren syndrome with dental involvement
- M35.1Other overlap syndromes
- M35.2Behcet's disease
- M35.3Polymyalgia rheumatica
- M35.4Diffuse (eosinophilic) fasciitis
- M35.5Multifocal fibrosclerosis
- M35.6Relapsing panniculitis [Weber-Christian]
- M35.7Hypermobility syndrome
- M35.8Other specified systemic involvement of connective tissue
- M35.81Multisystem inflammatory syndrome
- M35.89Other specified systemic involvement of connective tissue
- M35.9Systemic involvement of connective tissue, unspecified
- M36Systemic disorders of connective tissue in diseases classified elsewhere
- M36.0Dermato(poly)myositis in neoplastic disease
- M36.1Arthropathy in neoplastic disease
- M36.2Hemophilic arthropathy
- M36.3Arthropathy in other blood disorders
- M36.4Arthropathy in hypersensitivity reactions classified elsewhere
- M36.8Systemic disorders of connective tissue in other diseases classified elsewhere
M30-M36 MS-DRGs
This code does not group to an MS-DRG as a principal diagnosis.
Other codes that refer to M30-M36
Notes on these codes point to M30-M36.
- CH12 Excludes2: systemic connective tissue disorders (M30-M36)
- CH9 Excludes2: systemic connective tissue disorders (M30-M36)
- I77 Excludes2: collagen (vascular) diseases (M30-M36)
- J82 Excludes2: pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)
- J84.170 Code First: systemic connective tissue disorders (M30-M36)
- L94 Excludes1: systemic connective tissue disorders (M30-M36)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Vasculitis
Vasculitis is an inflammation of the blood vessels. It happens when the body's immune system attacks the blood vessel by mistake. It can happen because of an infection, a medicine, or another disease. The cause is often unknown.
Read more about vasculitis on MedlinePlus