Systemic sclerosis [scleroderma]
In Systemic connective tissue disorders (M30-M36), chapter 13: Diseases of the Musculoskeletal System and Connective Tissue
8 billable codes under M34: 2 are a CC; 7 map to HCC 93 (Rheumatoid Arthritis and Other Specified Inflammatory Rheumatic Disorders), HCC 278 (Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis).A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment. An HCC counts toward a Medicare Advantage patient's risk score.
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Instructional notes
Also applies, from Systemic connective tissue disorders (M30-M36)
These notes sit on M30-M36 and apply to every code under it, including M34.
Includes: conditions that are coded here
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes1: not coded here, use a different code
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers site and laterality, acute injury versus chronic musculoskeletal conditions, 7th characters for pathologic fractures, osteoporosis with or without current fracture, and multisystem inflammatory syndrome.
- Site and laterality (page 60)
- Acute traumatic versus chronic or recurrent musculoskeletal conditions (page 61)
- Coding of Pathologic Fractures (page 61)
- Osteoporosis (page 61)
- Multisystem Inflammatory Syndrome (page 62)
All codes under M34
M34 can't be used on a claim. Pick a billable code below; grey headings group them.
- M34.0Progressive systemic sclerosis
- M34.1CR(E)ST syndrome
- M34.2Systemic sclerosis induced by drug and chemical
- M34.8Other forms of systemic sclerosis
- M34.81Systemic sclerosis with lung involvement
- M34.82Systemic sclerosis with myopathy
- M34.83Systemic sclerosis with polyneuropathy
- M34.89Other systemic sclerosis
- M34.9Systemic sclerosis, unspecified
M34 MS-DRGs
As the principal diagnosis, the billable codes under M34 group to these 8 MS-DRGs (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 545 Connective Tissue Disorders with MCC (6 of 8 codes)
- DRG 546 Connective Tissue Disorders with CC (6 of 8 codes)
- DRG 547 Connective Tissue Disorders without CC/MCC (6 of 8 codes)
- DRG 073 Cranial and Peripheral Nerve Disorders with MCC (1 of 8 codes)
- DRG 074 Cranial and Peripheral Nerve Disorders without MCC (1 of 8 codes)
- DRG 196 Interstitial Lung Disease with MCC (1 of 8 codes)
- DRG 197 Interstitial Lung Disease with CC (1 of 8 codes)
- DRG 198 Interstitial Lung Disease without CC/MCC (1 of 8 codes)
Other codes that refer to M34
Notes on these codes point to M34.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Scleroderma
Scleroderma means "hard skin." It's the name of an autoimmune disease that causes inflammation and thickening in the skin and other areas of the body. This inflammation causes you to have areas of tight, hard skin. Scleroderma may affect just one area of your body, or it can affect many systems in your body.
Read more about scleroderma on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
