Polyarteritis nodosa and related conditions
In Systemic connective tissue disorders (M30-M36), chapter 13: Diseases of the Musculoskeletal System and Connective Tissue
5 billable codes under M30: all are a CC; all map to HCC 94 (Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders), HCC 93 (Rheumatoid Arthritis and Other Specified Inflammatory Rheumatic Disorders), HCC 278 (Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis).A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment. An HCC counts toward a Medicare Advantage patient's risk score.
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Instructional notes
Excludes1: not coded here, use a different code
- microscopic polyarteritis (M31.7)
Also applies, from Systemic connective tissue disorders (M30-M36)
These notes sit on M30-M36 and apply to every code under it, including M30.
Includes: conditions that are coded here
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes1: not coded here, use a different code
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers site and laterality, acute injury versus chronic musculoskeletal conditions, 7th characters for pathologic fractures, osteoporosis with or without current fracture, and multisystem inflammatory syndrome.
- Site and laterality (page 60)
- Acute traumatic versus chronic or recurrent musculoskeletal conditions (page 61)
- Coding of Pathologic Fractures (page 61)
- Osteoporosis (page 61)
- Multisystem Inflammatory Syndrome (page 62)
All codes under M30
M30 can't be used on a claim. Pick a billable code below; grey headings group them.
M30 MS-DRGs
As the principal diagnosis, the billable codes under M30 group to MS-DRG 545, 546, 547, 542, 543, or 544 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
- DRG 545 Connective Tissue Disorders with MCC (4 of 5 codes)
- DRG 546 Connective Tissue Disorders with CC (4 of 5 codes)
- DRG 547 Connective Tissue Disorders without CC/MCC (4 of 5 codes)
- DRG 542 Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with MCC (1 of 5 codes)
- DRG 543 Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with CC (1 of 5 codes)
- DRG 544 Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy without CC/MCC (1 of 5 codes)
Other codes that refer to M30
Notes on these codes point to M30.
- CH12 Excludes2: systemic connective tissue disorders (M30-M36)
- CH9 Excludes2: systemic connective tissue disorders (M30-M36)
- I77 Excludes2: collagen (vascular) diseases (M30-M36)
- J82 Excludes2: pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)
- J84.170 Code First: systemic connective tissue disorders (M30-M36)
- L94 Excludes1: systemic connective tissue disorders (M30-M36)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Vasculitis
Vasculitis is an inflammation of the blood vessels. It happens when the body's immune system attacks the blood vessel by mistake. It can happen because of an infection, a medicine, or another disease. The cause is often unknown.
Read more about vasculitis on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
