All ICD10 Codes
Chapter 9

I00–I99: Diseases of the Circulatory System

Diseases of the Circulatory System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)
All CodesBillable Only
Internal Codes
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  • I26.04—

    Fat embolism of pulmonary artery with acute cor pulmonale

  • I26.09—

    Other pulmonary embolism with acute cor pulmonale

  • I26.90—

    Septic pulmonary embolism without acute cor pulmonale

  • I26.92—

    Saddle embolus of pulmonary artery without acute cor pulmonale

  • I26.93—

    Single subsegmental thrombotic pulmonary embolism without acute cor pulmonale

  • I26.94—

    Multiple subsegmental thrombotic pulmonary emboli without acute cor pulmonale

  • I26.95—

    Cement embolism of pulmonary artery without acute cor pulmonale

  • I26.96—

    Fat embolism of pulmonary artery without acute cor pulmonale

  • I26.99—

    Other pulmonary embolism without acute cor pulmonale

  • I27.0—

    Primary pulmonary hypertension

  • I27.1—

    Kyphoscoliotic heart disease

  • I27.20—

    Pulmonary hypertension, unspecified

  • I27.21—

    Secondary pulmonary arterial hypertension

  • I27.22—

    Pulmonary hypertension due to left heart disease

  • I27.23—

    Pulmonary hypertension due to lung diseases and hypoxia

  • I27.24—

    Chronic thromboembolic pulmonary hypertension

  • I27.29—

    Other secondary pulmonary hypertension

  • I27.81—

    Cor pulmonale (chronic)

  • I27.82—

    Chronic pulmonary embolism

  • I27.83—

    Eisenmenger's syndrome

  • I27.840—

    Fontan-associated liver disease [FALD]

  • I27.841—

    Fontan-associated lymphatic dysfunction

  • I27.848—

    Other Fontan-associated condition

  • I27.849—

    Fontan related circulation, unspecified

  • I27.89—

    Other specified pulmonary heart diseases

  • I27.9—

    Pulmonary heart disease, unspecified

  • I28.0—

    Arteriovenous fistula of pulmonary vessels

  • I28.1—

    Aneurysm of pulmonary artery

  • I28.8—

    Other diseases of pulmonary vessels

  • I28.9—

    Disease of pulmonary vessels, unspecified

  • I30.0—

    Acute nonspecific idiopathic pericarditis

  • I30.1—

    Infective pericarditis

  • I30.8—

    Other forms of acute pericarditis

  • I30.9—

    Acute pericarditis, unspecified

  • I31.0—

    Chronic adhesive pericarditis

  • I31.1—

    Chronic constrictive pericarditis

  • I31.2—

    Hemopericardium, not elsewhere classified

  • I31.31—

    Malignant pericardial effusion in diseases classified elsewhere

  • I31.39—

    Other pericardial effusion (noninflammatory)

  • I31.4—

    Cardiac tamponade

  • I31.8—

    Other specified diseases of pericardium

  • I31.9—

    Disease of pericardium, unspecified

  • I32—

    Pericarditis in diseases classified elsewhere

  • I33.0—

    Acute and subacute infective endocarditis

  • I33.9—

    Acute and subacute endocarditis, unspecified

  • I34.0—

    Nonrheumatic mitral (valve) insufficiency

  • I34.1—

    Nonrheumatic mitral (valve) prolapse

  • I34.2—

    Nonrheumatic mitral (valve) stenosis

  • I34.81—

    Nonrheumatic mitral (valve) annulus calcification

  • I34.89—

    Other nonrheumatic mitral valve disorders

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