I27.841

Billable

ChapterI00–I99

Ranksubcategory

Official Description

Fontan-associated lymphatic dysfunction

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 9: Diseases of the Circulatory System (I00-I99).

Instructional Notes

Code Also

associated conditions such as:
chylothorax (J94.0)
Fontan associated protein-losing enteropathy (K90.49)
plastic (obstructive) bronchitis (J44.89)

General instructions are available for the parent sections:

View CH9 Notes

Clinical Hierarchy

CH9Diseases of the circulatory system (I00-I99)

I26-I28Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

I27Other pulmonary heart diseases

I27.8Other specified pulmonary heart diseases

I27.84Fontan related circulation

I27.841Fontan-associated lymphatic dysfunction

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to I27.841:

chapterCH9

Diseases of the circulatory system (I00-I99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to I27.841. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

2 raw paths

Circulation1 unique routes

Fontan related

with

Fontan-associated lymphatic dysfunction→I27.841

Dysfunction1 unique routes

lymphatic

Fontan-associated→I27.841

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 808

Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC

DRG 809

Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC

DRG 810

Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Cross Reference

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