I27

Non-Billable

ChapterI00–I99

Rankcategory

Official Description

Other pulmonary heart diseases

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 9: Diseases of the Circulatory System (I00-I99).

CH9 Parent Instructions

Excludes2(Not included here)

certain conditions originating in the perinatal period (P04-P96)
certain infectious and parasitic diseases (A00-B99)
complications of pregnancy, childbirth and the puerperium (O00-O9A)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
endocrine, nutritional and metabolic diseases (E00-E88)
injury, poisoning and certain other consequences of external causes (S00-T88)
neoplasms (C00-D49)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
systemic connective tissue disorders (M30-M36)
transient cerebral ischemic attacks and related syndromes (G45.-)

Clinical Hierarchy

CH9Diseases of the circulatory system (I00-I99)

I26-I28Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

I27Other pulmonary heart diseases

I27.0Primary pulmonary hypertension

I27.1Kyphoscoliotic heart disease

I27.2Other secondary pulmonary hypertension

I27.8Other specified pulmonary heart diseases

I27.9Pulmonary heart disease, unspecified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to I27:

chapterCH9

Diseases of the circulatory system (I00-I99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to I27. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

25 raw paths

Arrillaga-Ayerza syndrome (pulmonary sclerosis with pulmonary hypertension)1 unique routes

Direct index entry→I27

Arteriosclerosis, arteriosclerotic (diffuse) (obliterans) (of) (senile) (with calcification)1 unique routes

pulmonary (idiopathic)→I27

Ayerza's disease or syndrome (pulmonary artery sclerosis with pulmonary hypertension)1 unique routes

Direct index entry→I27

Cardiopathia nigra1 unique routes

Direct index entry→I27

Circulation4 unique routes

Fontan related→I27(4 variants)

with(3 variants)