Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G40.109

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus

  • G40.11

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable

  • G40.111

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus

  • G40.119

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus

  • G40.2

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

  • G40.20

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable

  • G40.201

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus

  • G40.209

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus

  • G40.21

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable

  • G40.211

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus

  • G40.219

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus

  • G40.3

    Generalized idiopathic epilepsy and epileptic syndromes

  • G40.30

    Generalized idiopathic epilepsy and epileptic syndromes, not intractable

  • G40.301

    Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus

  • G40.309

    Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus

  • G40.31

    Generalized idiopathic epilepsy and epileptic syndromes, intractable

  • G40.311

    Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus

  • G40.319

    Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus

  • G40.4

    Other generalized epilepsy and epileptic syndromes

  • G40.40

    Other generalized epilepsy and epileptic syndromes, not intractable

  • G40.401

    Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus

  • G40.409

    Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus

  • G40.41

    Other generalized epilepsy and epileptic syndromes, intractable

  • G40.411

    Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus

  • G40.419

    Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus

  • G40.42

    Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

  • G40.5

    Epileptic seizures related to external causes

  • G40.50

    Epileptic seizures related to external causes, not intractable

  • G40.501

    Epileptic seizures related to external causes, not intractable, with status epilepticus

  • G40.509

    Epileptic seizures related to external causes, not intractable, without status epilepticus

  • G40.8

    Other epilepsy and recurrent seizures

  • G40.80

    Other epilepsy

  • G40.801

    Other epilepsy, not intractable, with status epilepticus

  • G40.802

    Other epilepsy, not intractable, without status epilepticus

  • G40.803

    Other epilepsy, intractable, with status epilepticus

  • G40.804

    Other epilepsy, intractable, without status epilepticus

  • G40.81

    Lennox-Gastaut syndrome

  • G40.811

    Lennox-Gastaut syndrome, not intractable, with status epilepticus

  • G40.812

    Lennox-Gastaut syndrome, not intractable, without status epilepticus

  • G40.813

    Lennox-Gastaut syndrome, intractable, with status epilepticus

  • G40.814

    Lennox-Gastaut syndrome, intractable, without status epilepticus

  • G40.82

    Epileptic spasms

  • G40.821

    Epileptic spasms, not intractable, with status epilepticus

  • G40.822

    Epileptic spasms, not intractable, without status epilepticus

  • G40.823

    Epileptic spasms, intractable, with status epilepticus

  • G40.824

    Epileptic spasms, intractable, without status epilepticus

  • G40.83

    Dravet syndrome

  • G40.833

    Dravet syndrome, intractable, with status epilepticus

  • G40.834

    Dravet syndrome, intractable, without status epilepticus

  • G40.84

    KCNQ2-related epilepsy

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