Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G40.841

    KCNQ2-related epilepsy, not intractable, with status epilepticus

  • G40.842

    KCNQ2-related epilepsy, not intractable, without status epilepticus

  • G40.843

    KCNQ2-related epilepsy, intractable, with status epilepticus

  • G40.844

    KCNQ2-related epilepsy, intractable, without status epilepticus

  • G40.89

    Other seizures

  • G40.9

    Epilepsy, unspecified

  • G40.90

    Epilepsy, unspecified, not intractable

  • G40.901

    Epilepsy, unspecified, not intractable, with status epilepticus

  • G40.909

    Epilepsy, unspecified, not intractable, without status epilepticus

  • G40.91

    Epilepsy, unspecified, intractable

  • G40.911

    Epilepsy, unspecified, intractable, with status epilepticus

  • G40.919

    Epilepsy, unspecified, intractable, without status epilepticus

  • G40.A

    Absence epileptic syndrome

  • G40.A0

    Absence epileptic syndrome, not intractable

  • G40.A01

    Absence epileptic syndrome, not intractable, with status epilepticus

  • G40.A09

    Absence epileptic syndrome, not intractable, without status epilepticus

  • G40.A1

    Absence epileptic syndrome, intractable

  • G40.A11

    Absence epileptic syndrome, intractable, with status epilepticus

  • G40.A19

    Absence epileptic syndrome, intractable, without status epilepticus

  • G40.B

    Juvenile myoclonic epilepsy [impulsive petit mal]

  • G40.B0

    Juvenile myoclonic epilepsy, not intractable

  • G40.B01

    Juvenile myoclonic epilepsy, not intractable, with status epilepticus

  • G40.B09

    Juvenile myoclonic epilepsy, not intractable, without status epilepticus

  • G40.B1

    Juvenile myoclonic epilepsy, intractable

  • G40.B11

    Juvenile myoclonic epilepsy, intractable, with status epilepticus

  • G40.B19

    Juvenile myoclonic epilepsy, intractable, without status epilepticus

  • G40.C

    Lafora progressive myoclonus epilepsy

  • G40.C0

    Lafora progressive myoclonus epilepsy, not intractable

  • G40.C01

    Lafora progressive myoclonus epilepsy, not intractable, with status epilepticus

  • G40.C09

    Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus

  • G40.C1

    Lafora progressive myoclonus epilepsy, intractable

  • G40.C11

    Lafora progressive myoclonus epilepsy, intractable, with status epilepticus

  • G40.C19

    Lafora progressive myoclonus epilepsy, intractable, without status epilepticus

  • G43

    Migraine

  • G43.0

    Migraine without aura

  • G43.00

    Migraine without aura, not intractable

  • G43.001

    Migraine without aura, not intractable, with status migrainosus

  • G43.009

    Migraine without aura, not intractable, without status migrainosus

  • G43.01

    Migraine without aura, intractable

  • G43.011

    Migraine without aura, intractable, with status migrainosus

  • G43.019

    Migraine without aura, intractable, without status migrainosus

  • G43.1

    Migraine with aura

  • G43.10

    Migraine with aura, not intractable

  • G43.101

    Migraine with aura, not intractable, with status migrainosus

  • G43.109

    Migraine with aura, not intractable, without status migrainosus

  • G43.11

    Migraine with aura, intractable

  • G43.111

    Migraine with aura, intractable, with status migrainosus

  • G43.119

    Migraine with aura, intractable, without status migrainosus

  • G43.4

    Hemiplegic migraine

  • G43.40

    Hemiplegic migraine, not intractable

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