All ICD10 Codes

G40.42

Billable
ChapterG00–G99
Ranksubcategory
Official Description

Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes
  • CDKL5
Use Additional Code
  • code, if known, to identify associated manifestations, such as:
  • cortical blindness (H47.61-)
  • global developmental delay (F88)
General instructions are available for the parent sections:
View CH6 NotesView G40 NotesView G40.4 Notes

Clinical Hierarchy

BillableHas subcodes
CH6Diseases of the nervous system (G00-G99)
G40-G47Episodic and paroxysmal disorders (G40-G47)
G40Epilepsy and recurrent seizures
G40.4Other generalized epilepsy and epileptic syndromes
G40.42Cyclin-Dependent Kinase-Like 5 Deficiency DisorderBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G40.42:

subcategoryG40.4
Other generalized epilepsy and epileptic syndromes
View context instructions
categoryG40
Epilepsy and recurrent seizures
View context instructions
chapterCH6
Diseases of the nervous system (G00-G99)
View context instructions

Code History

  • FY 2020: This code replaced G40.89 (Other seizures)

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 023
Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator
DRG 100
Seizures with MCC
DRG 101
Seizures without MCC

Cross Reference

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