All ICD10 Codes
Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All CodesBillable Only
Internal Codes
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  • E78.00—

    Pure hypercholesterolemia, unspecified

  • E78.010—

    Homozygous familial hypercholesterolemia [HoFH]

  • E78.011—

    Heterozygous familial hypercholesterolemia [HeFH]

  • E78.019—

    Familial hypercholesterolemia, unspecified

  • E78.1—

    Pure hyperglyceridemia

  • E78.2—

    Mixed hyperlipidemia

  • E78.3—

    Hyperchylomicronemia

  • E78.41—

    Elevated Lipoprotein(a)

  • E78.49—

    Other hyperlipidemia

  • E78.5—

    Hyperlipidemia, unspecified

  • E78.6—

    Lipoprotein deficiency

  • E78.70—

    Disorder of bile acid and cholesterol metabolism, unspecified

  • E78.71—

    Barth syndrome

  • E78.72—

    Smith-Lemli-Opitz syndrome

  • E78.79—

    Other disorders of bile acid and cholesterol metabolism

  • E78.81—

    Lipoid dermatoarthritis

  • E78.89—

    Other lipoprotein metabolism disorders

  • E78.9—

    Disorder of lipoprotein metabolism, unspecified

  • E79.0—

    Hyperuricemia without signs of inflammatory arthritis and tophaceous disease

  • E79.1—

    Lesch-Nyhan syndrome

  • E79.2—

    Myoadenylate deaminase deficiency

  • E79.81—

    Aicardi-Goutières syndrome

  • E79.82—

    Hereditary xanthinuria

  • E79.89—

    Other specified disorders of purine and pyrimidine metabolism

  • E79.9—

    Disorder of purine and pyrimidine metabolism, unspecified

  • E80.0—

    Hereditary erythropoietic porphyria

  • E80.1—

    Porphyria cutanea tarda

  • E80.20—

    Unspecified porphyria

  • E80.21—

    Acute intermittent (hepatic) porphyria

  • E80.29—

    Other porphyria

  • E80.3—

    Defects of catalase and peroxidase

  • E80.4—

    Gilbert syndrome

  • E80.5—

    Crigler-Najjar syndrome

  • E80.6—

    Other disorders of bilirubin metabolism

  • E80.7—

    Disorder of bilirubin metabolism, unspecified

  • E83.00—

    Disorder of copper metabolism, unspecified

  • E83.01—

    Wilson's disease

  • E83.09—

    Other disorders of copper metabolism

  • E83.10—

    Disorder of iron metabolism, unspecified

  • E83.110—

    Hereditary hemochromatosis

  • E83.111—

    Hemochromatosis due to repeated red blood cell transfusions

  • E83.118—

    Other hemochromatosis

  • E83.119—

    Hemochromatosis, unspecified

  • E83.19—

    Other disorders of iron metabolism

  • E83.2—

    Disorders of zinc metabolism

  • E83.30—

    Disorder of phosphorus metabolism, unspecified

  • E83.31—

    Familial hypophosphatemia

  • E83.32—

    Hereditary vitamin D-dependent rickets (type 1) (type 2)

  • E83.39—

    Other disorders of phosphorus metabolism

  • E83.40—

    Disorders of magnesium metabolism, unspecified

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