All ICD10 Codes

E88.89

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Other specified metabolic disorders

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Launois-Bensaude adenolipomatosis
Excludes1(Not coded here)
  • adult pulmonary Langerhans cell histiocytosis (J84.82)
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E88 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E88Other and unspecified metabolic disorders
E88.8Other specified metabolic disorders
E88.89Other specified metabolic disorders

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E88.89:

categoryE88
Other and unspecified metabolic disorders
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E88.89. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

15 raw paths
Adenolipomatosis, Launois-Bensaude1 unique routes
Direct index entry→E88.89
Deficiency, deficient1 unique routes
dihydropyrimidine dehydrogenase (DPD)→E88.89
Dihydropyrimidine dehydrogenase disease (DPD)1 unique routes
Direct index entry→E88.89
Disease, diseased1 unique routes
Erdheim-Chester (ECD)→E88.89
Disorder (of)1 unique routes
metabolism NOS
specified NEC→E88.89
DPD (dihydropyrimidine dehydrogenase deficiency)1 unique routes
Direct index entry→E88.89
Hoffa-Kastert disease1 unique routes
Direct index entry→E88.89
Hoffa's disease1 unique routes
Direct index entry→E88.89
Ketosis NEC1 unique routes
Direct index entry→E88.89
Launois-Bensaude adenolipomatosis1 unique routes
Direct index entry→E88.89
Lipomatosis1 unique routes
Launois-Bensaude→E88.89
Liposynovitis prepatellaris1 unique routes
Direct index entry→E88.89
Madelung's1 unique routes
disease
symmetrical lipomas, neck→E88.89
Steatosis1 unique routes
Direct index entry→E88.89
Syndrome1 unique routes
Erdheim-Chester (ECD)→E88.89

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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