E76Not billable, use a more specific code below

Disorders of glycosaminoglycan metabolism

In Metabolic disorders (E70-E88), chapter 4: Endocrine, Nutritional and Metabolic Diseases

12 billable codes under E76: all are a CC; 10 map to HCC 49 (Specified Lysosomal Storage Disorders).A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment. An HCC counts toward a Medicare Advantage patient's risk score.

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Instructional notes

Also applies, from Metabolic disorders (E70-E88)

These notes sit on E70-E88 and apply to every code under it, including E76.

Excludes1: not coded here, use a different code

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2: not included here, code separately if applicable

  • Ehlers-Danlos syndromes (Q79.6-)

Official coding guidelines

From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.

Covers diabetes mellitus coding, including type, insulin and drug use, pump malfunction and secondary diabetes, plus obesity and obesity class codes.

Read Section I.C.4 (page 39)

E76 MS-DRG

As the principal diagnosis, all 12 billable codes under E76 group to MS-DRG 642 (v44.0).

About the condition

Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.

Carbohydrate Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Read more about carbohydrate metabolism disorders on MedlinePlus

Code history

Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.