All ICD10 Codes

E76

Non-Billable
ChapterE00–E89
Rankcategory
Official Description

Disorders of glycosaminoglycan metabolism

Use a more specific code (4 billable, 2 non-billable)
E76.0Mucopolysaccharidosis, type Ihas subcodesE76.1Mucopolysaccharidosis, type IIE76.2Other mucopolysaccharidoseshas subcodesE76.3Mucopolysaccharidosis, unspecifiedE76.8Other disorders of glucosaminoglycan metabolismE76.9Glucosaminoglycan metabolism disorder, unspecified
Metadata & Insights
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

CH4 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

E70-E88 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2(Not included here. Code separately if applicable.)
  • Ehlers-Danlos syndromes (Q79.6-)

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E76Disorders of glycosaminoglycan metabolismNot billable
E76.0Mucopolysaccharidosis, type ISubcodes
E76.1Mucopolysaccharidosis, type IIBillable
E76.2Other mucopolysaccharidosesSubcodes
E76.3Mucopolysaccharidosis, unspecifiedBillable
E76.8Other disorders of glucosaminoglycan metabolismBillable
E76.9Glucosaminoglycan metabolism disorder, unspecifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E76:

blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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