Disseminated intravascular coagulation [defibrination syndrome]
In Coagulation defects, purpura and other hemorrhagic conditions (D65-D69), chapter 3: Diseases of the Blood and Blood-Forming Organs
- D65 is billable and valid on claims for FY 2027. If the record has more detail, check the other codes under D65-D69 below.
- As a secondary diagnosis it is an MCC (major complication), which can raise the MS-DRG payment. It doesn't count when the principal diagnosis is one of 51 closely related codes.
- Doesn't count toward a Medicare Advantage risk score (no HCC in V28; it was HCC 48 in V24).
- AHRQ's Chronic Condition Indicator classes it as not chronic (an acute or short-term condition).
- 610 US deaths in 2024 had an underlying cause in category D65, per the National Vital Statistics System on CDC WONDER. Death records use WHO ICD-10, so the count is for the whole category.
Also indexed as: Absence, fibrinogen, acquired; Afibrinogenemia, acquired; Coagulation, COVID-19 associated; Coagulopathy, consumption; Coagulopathy, intravascular; Defibrination; Deficiency, fibrinogen, acquired; Disorder, glomerular, disseminated intravascular coagulation; Fibrinogenopenia, acquired; Fibrinolysis; Glomerulonephritis, in, defibrination syndrome; Glomerulonephritis, in, disseminated intravascular coagulation; Hypofibrinogenemia, acquired; Proteolysis; Purpura, fulminans, fulminous; Purpura, gangrenous; Syndrome, DIC; Syndrome, ICF; Syndrome, intravascular coagulation-fibrinolysis; Syndrome, IVC
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Instructional notes
Includes: conditions that are coded here
- Afibrinogenemia, acquired
- Consumption coagulopathy
- COVID-19 associated diffuse or disseminated intravascular coagulopathy
- Diffuse or disseminated intravascular coagulation [DIC]
- Fibrinolytic hemorrhage, acquired
- Fibrinolytic purpura
- Purpura fulminans
Excludes1: not coded here, use a different code
Excludes2: not included here, code separately if applicable
Code also: add a code for this too, order depends on the encounter
- if applicable, associated condition
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
There are no chapter-specific rules for Chapter 3 yet, so the general rules in Section I.B apply.
Other codes under D65-D69
Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
- D65Disseminated intravascular coagulation [defibrination syndrome](this code)
- D66Hereditary factor VIII deficiency
- D67Hereditary factor IX deficiency
- D68Other coagulation defects
- D69Purpura and other hemorrhagic conditions
D65 MS-DRGs
As the principal diagnosis, D65 groups to MS-DRG 791, 793, or 813 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
Related conditions
Grouped by AHRQ's Clinical Classifications Software Refined (CCSR), which sorts every diagnosis code into clinically meaningful categories.
D65 is in Coagulation and hemorrhagic disorders (BLD006, its default category), with 49 codes. Others in it:
- D47.3 Essential (hemorrhagic) thrombocythemia
- D66 Hereditary factor VIII deficiency
- D67 Hereditary factor IX deficiency
- D68.00 Von Willebrand disease, unspecified
- D68.01 Von Willebrand disease, type 1
- D68.020 Von Willebrand disease, type 2A
- D68.021 Von Willebrand disease, type 2B
- D68.022 Von Willebrand disease, type 2M
Medicare coverage articles listing D65
This Medicare billing and coding article lists D65 as a diagnosis that supports medical necessity for the services they cover. From the CMS Medicare Coverage Database; check your own contractor's article before billing.
Other codes that refer to D65
Notes on these codes point to D65.
- D68.6 Excludes1: diffuse or disseminated intravascular coagulation [DIC] (D65)
- D69 Excludes1: purpura fulminans (D65)
- G90.81 Use Additional Code: disseminated intravascular coagulation (D65)
- N08 Code First: disseminated intravascular coagulation (D65)
- O99.1 Includes: Conditions in D65-D89
- R65.11 Use Additional Code: disseminated intravascular coagulopathy [DIC] (D65)
- R65.2 Use Additional Code: disseminated intravascular coagulopathy [DIC] (D65)
- R70-R79 Excludes2: coagulation hemorrhagic disorders (D65-D68)
- U07.1 Use Additional Code: disseminated intravascular coagulation (D65)
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Bleeding Disorders
Normally, if you get hurt, your body forms a blood clot to stop the bleeding. For blood to clot, your body needs cells called platelets and proteins known as clotting factors. If you have a bleeding disorder, you either do not have enough platelets or clotting factors or they don't work the way they should.
Read more about bleeding disorders on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
ICD-9-CM equivalent
Legacy crosswalk from the CMS General Equivalence Mappings (last updated 2018).
- 286.6 Defibrination syndrome