All ICD10 Codes

D55.1

Billable
ChapterD50–D89
Ranksubcategory
Official Description

Anemia due to other disorders of glutathione metabolism

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Includes
  • Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
  • Anemia (due to) hemolytic nonspherocytic (hereditary), type I
General instructions are available for the parent sections:
View CH3 NotesView D55 Notes

Clinical Hierarchy

CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D55-D59Hemolytic anemias (D55-D59)
D55Anemia due to enzyme disorders
D55.1Anemia due to other disorders of glutathione metabolism

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D55.1:

categoryD55
Anemia due to enzyme disorders
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to D55.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

14 raw paths
Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)13 unique routes
deficiency(7 variants)
6 phosphogluconate dehydrogenase→D55.1
6-PGD→D55.1
enzyme
related to hexose monophosphate (HMP) shunt pathway NEC→D55.1
erythrocytic glutathione→D55.1
G SH→D55.1
GGS-R→D55.1
glutathione reductase→D55.1
due to (in) (with)
disorder of
glutathione metabolism→D55.1
erythrocytic glutathione deficiency→D55.1
glutathione-reductase deficiency→D55.1
hemolytic(2 variants)
nonspherocytic(2 variants)
congenital or hereditary NEC
type
I→D55.1
type
I→D55.1
with (due to) (in)
disorder of
pentose phosphate pathway→D55.1
Disorder (of)1 unique routes
pentose phosphate pathway with anemia→D55.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 811
Red Blood Cell Disorders with MCC
DRG 812
Red Blood Cell Disorders without MCC

Cross Reference

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